ABCDEFGHIJKLMNOPQRSTUVWXYZ
1
Gene Protein Name
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AASSAlpha-aminoadipic semialdehyde synthase, mitochondrial (LKR/SDH) [Includes: Lysine ketoglutarate reductase (LKR) (LOR) (EC 1.5.1.8); Saccharopine dehydrogenase (SDH) (EC 1.5.1.9)]
3
ACMSD2-amino-3-carboxymuconate-6-semialdehyde decarboxylase (EC 4.1.1.45) (Picolinate carboxylase)
4
ADH1A ADH1Alcohol dehydrogenase 1A (EC 1.1.1.1) (Alcohol dehydrogenase subunit alpha)
5
ADH1B ADH2Alcohol dehydrogenase 1B (EC 1.1.1.1) (Alcohol dehydrogenase subunit beta)
6
ADH1C ADH3Alcohol dehydrogenase 1C (EC 1.1.1.1) (Alcohol dehydrogenase subunit gamma)
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ADH4Alcohol dehydrogenase 4 (EC 1.1.1.1) (Alcohol dehydrogenase class II pi chain)
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ADH5 ADHX FDHAlcohol dehydrogenase class-3 (EC 1.1.1.1) (Alcohol dehydrogenase class-III) (Alcohol dehydrogenase 5) (Alcohol dehydrogenase class chi chain) (S-(hydroxymethyl)glutathione dehydrogenase) (EC 1.1.1.284) (Glutathione-dependent formaldehyde dehydrogenase) (GSH-FDH) (FALDH) (FDH) (EC 1.1.1.-)
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ADH6Alcohol dehydrogenase 6 (EC 1.1.1.1)
11
ADH7Alcohol dehydrogenase class 4 mu/sigma chain (EC 1.1.1.1) (Alcohol dehydrogenase class IV mu/sigma chain) (Retinol dehydrogenase) (Gastric alcohol dehydrogenase)
13
AFMIDProbable arylformamidase (EC 3.5.1.9) (Kynurenine formamidase) (KF)
14
AHCY SAHHAdenosylhomocysteinase (AdoHcyase) (EC 3.3.1.1) (S-adenosyl-L-homocysteine hydrolase)
15
AHCYL1 DCAL XPVKONAPutative adenosylhomocysteinase 2 (AdoHcyase 2) (EC 3.3.1.1) (S-adenosyl-L-homocysteine hydrolase 2) (S-adenosylhomocysteine hydrolase-like protein 1) (DC-expressed AHCY-like molecule)
16
AHCYL2 KIAA0828Putative adenosylhomocysteinase 3 (AdoHcyase 3) (EC 3.3.1.1) (S-adenosyl-L-homocysteine hydrolase 3) (S-adenosylhomocysteine hydrolase-like protein 2)
18
AKR1A1 ALDR1 ALRAlcohol dehydrogenase [NADP+] (EC 1.1.1.2) (Aldehyde reductase) (Aldo-keto reductase family 1 member A1)
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AKR1B1 ALDR1Aldose reductase (AR) (EC 1.1.1.21) (Aldehyde reductase) (Aldo-keto reductase family 1 member B1)
21
AKR1C1 DDH DDH1Aldo-keto reductase family 1 member C1 (EC 1.1.1.-) (20-alpha-hydroxysteroid dehydrogenase) (20-alpha-HSD) (EC 1.1.1.149) (Trans-1,2-dihydrobenzene-1,2-diol dehydrogenase) (EC 1.3.1.20) (Indanol dehydrogenase) (EC 1.1.1.112) (Dihydrodiol dehydrogenase 1/2) (DD1/DD2) (Chlordecone reductase homolog HAKRC) (High-affinity hepatic bile acid-binding protein) (HBAB)
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AKR1C2 DDH2Aldo-keto reductase family 1 member C2 (EC 1.-.-.-) (Trans-1,2-dihydrobenzene-1,2-diol dehydrogenase) (EC 1.3.1.20) (Type III 3-alpha-hydroxysteroid dehydrogenase) (EC 1.1.1.213) (3-alpha-HSD3) (Dihydrodiol dehydrogenase 2) (DD-2) (DD2) (Dihydrodiol dehydrogenase/bile acid-binding protein) (DD/BABP) (Chlordecone reductase homolog HAKRD)
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AKR1C3 DDH1 HSD17B5 KIAA0119 PGFSAldo-keto reductase family 1 member C3 (EC 1.-.-.-) (Trans-1,2-dihydrobenzene-1,2-diol dehydrogenase) (EC 1.3.1.20) (3-alpha-hydroxysteroid dehydrogenase type 2) (3-alpha-HSD type 2) (EC 1.1.1.213) (3-alpha-HSD type II, brain) (Testosterone 17-beta-dehydrogenase 5) (EC 1.1.1.63) (EC 1.1.1.64) (17-beta-hydroxysteroid dehydrogenase type 5) (17-beta-HSD 5) (Prostaglandin F synthase) (PGFS) (EC 1.1.1.188) (Indanol dehydrogenase) (EC 1.1.1.112) (Dihydrodiol dehydrogenase type I) (Dihydrodiol dehydrogenase 3) (DD-3) (DD3) (Chlordecone reductase homolog HAKRb) (HA1753)
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AKR1C4 CHDRAldo-keto reductase family 1 member C4 (EC 1.1.1.-) (Chlordecone reductase) (CDR) (EC 1.1.1.225) (3-alpha-hydroxysteroid dehydrogenase type I) (EC 1.1.1.50) (3-alpha-HSD1) (Dihydrodiol dehydrogenase 4) (DD-4) (DD4) (HAKRA)
26
AKR1D1 SRD5B13-oxo-5-beta-steroid 4-dehydrogenase (EC 1.3.1.3) (Delta(4)-3-ketosteroid 5-beta-reductase) (Delta(4)-3-oxosteroid 5-beta-reductase) (Aldo-keto reductase family 1 member D1)
27
AKR1E2 AKR1CL2 AKRDC11,5-anhydro-D-fructose reductase (AF reductase) (EC 1.1.1.263) (Aldo-keto reductase family 1 member C-like protein 2) (Aldo-keto reductase family 1 member E2) (Testis-specific protein) (hTSP) (LoopADR)
28
AKR7A2 AFAR AFAR1 AKR7Aflatoxin B1 aldehyde reductase member 2 (EC 1.1.1.n11) (Succinic semialdehyde reductase) (SSA reductase) (AFB1 aldehyde reductase 1) (AFB1-AR 1) (Aldoketoreductase 7)
29
ALDH18A1 GSAS P5CS PYCSDelta-1-pyrroline-5-carboxylate synthase (P5CS) (Aldehyde dehydrogenase family 18 member A1) [Includes: Glutamate 5-kinase (GK) (EC 2.7.2.11) (Gamma-glutamyl kinase); Gamma-glutamyl phosphate reductase (GPR) (EC 1.2.1.41) (Glutamate-5-semialdehyde dehydrogenase) (Glutamyl-gamma-semialdehyde dehydrogenase)]
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ALDH1A1 ALDC ALDH1 PUMB1Retinal dehydrogenase 1 (RALDH 1) (RalDH1) (EC 1.2.1.36) (Aldehyde dehydrogenase family 1 member A1) (Aldehyde dehydrogenase, cytosolic) (ALHDII) (ALDH-E1)
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ALDH1A2 RALDH2Retinal dehydrogenase 2 (RALDH 2) (RalDH2) (EC 1.2.1.36) (Aldehyde dehydrogenase family 1 member A2) (Retinaldehyde-specific dehydrogenase type 2) (RALDH(II))
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ALDH1A3 ALDH6Aldehyde dehydrogenase family 1 member A3 (EC 1.2.1.5) (Aldehyde dehydrogenase 6) (Retinaldehyde dehydrogenase 3) (RALDH-3) (RalDH3)
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ALDH1B1 ALDH5 ALDHXAldehyde dehydrogenase X, mitochondrial (EC 1.2.1.3) (Aldehyde dehydrogenase family 1 member B1) (Aldehyde dehydrogenase 5)
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ALDH1L1 FTHFD10-formyltetrahydrofolate dehydrogenase (10-FTHFDH) (EC 1.5.1.6) (Aldehyde dehydrogenase family 1 member L1)
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ALDH1L2Probable 10-formyltetrahydrofolate dehydrogenase ALDH1L2 (EC 1.5.1.6) (Aldehyde dehydrogenase family 1 member L2)
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ALDH2 ALDMAldehyde dehydrogenase, mitochondrial (EC 1.2.1.3) (ALDH class 2) (ALDHI) (ALDH-E2)
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ALDH3A1 ALDH3Aldehyde dehydrogenase, dimeric NADP-preferring (EC 1.2.1.5) (Aldehyde dehydrogenase family 3 member A1) (Aldehyde dehydrogenase 3) (ALDHIII)
38
ALDH3A2 ALDH10 FALDHFatty aldehyde dehydrogenase (EC 1.2.1.3) (Aldehyde dehydrogenase family 3 member A2) (Aldehyde dehydrogenase 10) (Microsomal aldehyde dehydrogenase)
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ALDH3B1 ALDH7Aldehyde dehydrogenase family 3 member B1 (EC 1.2.1.5) (Aldehyde dehydrogenase 7)
40
ALDH3B2 ALDH8Aldehyde dehydrogenase family 3 member B2 (EC 1.2.1.5) (Aldehyde dehydrogenase 8)
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ALDH4A1 ALDH4 P5CDHDelta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (P5C dehydrogenase) (EC 1.5.1.12) (Aldehyde dehydrogenase family 4 member A1)
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ALDH5A1 SSADHSuccinate-semialdehyde dehydrogenase, mitochondrial (EC 1.2.1.24) (NAD(+)-dependent succinic semialdehyde dehydrogenase) (Aldehyde dehydrogenase family 5 member A1)
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ALDH6A1 MMSDHMethylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial (Malonate-semialdehyde dehydrogenase [acylating]) (MMSDH) (EC 1.2.1.27) (EC 1.2.1.18) (Aldehyde dehydrogenase family 6 member A1)
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ALDH7A1 ATQ1Alpha-aminoadipic semialdehyde dehydrogenase (Alpha-AASA dehydrogenase) (EC 1.2.1.31) (Betaine aldehyde dehydrogenase) (EC 1.2.1.8) (Delta1-piperideine-6-carboxylate dehydrogenase) (P6c dehydrogenase) (Aldehyde dehydrogenase family 7 member A1) (EC 1.2.1.3) (Antiquitin-1)
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ALDH8A1 ALDH12Aldehyde dehydrogenase family 8 member A1 (EC 1.2.1.-) (Aldehyde dehydrogenase 12)
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ALDH9A1 ALDH4 ALDH7 ALDH94-trimethylaminobutyraldehyde dehydrogenase (TMABADH) (EC 1.2.1.47) (Aldehyde dehydrogenase family 9 member A1) (EC 1.2.1.3) (Aldehyde dehydrogenase E3 isozyme) (Gamma-aminobutyraldehyde dehydrogenase) (EC 1.2.1.19) (R-aminobutyraldehyde dehydrogenase)
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ART1GPI-linked NAD(P)(+)--arginine ADP-ribosyltransferase 1 (EC 2.4.2.31) (Mono(ADP-ribosyl)transferase 1) (CD antigen CD296)
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ART3 TMARTEcto-ADP-ribosyltransferase 3 (EC 2.4.2.31) (NAD(P)(+)--arginine ADP-ribosyltransferase 3) (Mono(ADP-ribosyl)transferase 3)
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ART4 DO DOK1Ecto-ADP-ribosyltransferase 4 (EC 2.4.2.31) (NAD(P)(+)--arginine ADP-ribosyltransferase 4) (Mono(ADP-ribosyl)transferase 4) (Dombrock blood group carrier molecule) (CD antigen CD297)
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ART5 UNQ575/PRO1137Ecto-ADP-ribosyltransferase 5 (EC 2.4.2.31) (NAD(P)(+)--arginine ADP-ribosyltransferase 5) (Mono(ADP-ribosyl)transferase 5)
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ASPDHPutative L-aspartate dehydrogenase (EC 1.4.1.21) (Aspartate dehydrogenase domain-containing protein)
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ASPDHPutative L-aspartate dehydrogenase (EC 1.4.1.21) (Aspartate dehydrogenase domain-containing protein)
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BDH1 BDHD-beta-hydroxybutyrate dehydrogenase, mitochondrial (BDH) (EC 1.1.1.30) (3-hydroxybutyrate dehydrogenase)
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BDH2 DHRS6 UNQ6308/PRO209333-hydroxybutyrate dehydrogenase type 2 (EC 1.1.1.30) (R-beta-hydroxybutyrate dehydrogenase) (Dehydrogenase/reductase SDR family member 6) (Oxidoreductase UCPA)
60
BLVRA BLVR BVRBiliverdin reductase A (BVR A) (EC 1.3.1.24) (Biliverdin-IX alpha-reductase)
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BLVRB FLRFlavin reductase (FR) (EC 1.5.1.30) (NADPH-dependent diaphorase) (NADPH-flavin reductase) (FLR) (Biliverdin reductase B) (BVR-B) (EC 1.3.1.24) (Biliverdin-IX beta-reductase) (Green heme-binding protein) (GHBP)
62
BST1ADP-ribosyl cyclase 2 (EC 3.2.2.5) (Cyclic ADP-ribose hydrolase 2) (cADPr hydrolase 2) (Bone marrow stromal antigen 1) (BST-1) (CD antigen CD157)
63
C8orf38UPF0551 protein C8orf38, mitochondrial (Putative phytoene synthase)
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CATCatalase (EC 1.11.1.6)
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CBR1 CBR CRNCarbonyl reductase [NADPH] 1 (EC 1.1.1.184) (NADPH-dependent carbonyl reductase 1) (Prostaglandin-E(2) 9-reductase) (EC 1.1.1.189) (Prostaglandin 9-ketoreductase) (15-hydroxyprostaglandin dehydrogenase [NADP+]) (EC 1.1.1.197)
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CBR3Carbonyl reductase [NADPH] 3 (EC 1.1.1.184) (NADPH-dependent carbonyl reductase 3)
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CBR4Carbonyl reductase family member 4 (EC 1.-.-.-) (Quinone reductase CBR4) (3-oxoacyl-[acyl-carrier-protein] reductase) (EC 1.1.1.-)
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CD38ADP-ribosyl cyclase 1 (EC 3.2.2.5) (Cyclic ADP-ribose hydrolase 1) (cADPr hydrolase 1) (T10) (CD antigen CD38)
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CRYL1 CRYLambda-crystallin homolog (EC 1.1.1.45) (L-gulonate 3-dehydrogenase) (Gul3DH)
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CRYZQuinone oxidoreductase (EC 1.6.5.5) (NADPH:quinone reductase) (Zeta-crystallin)
73
CTBP1 CTBPC-terminal-binding protein 1 (CtBP1) (EC 1.1.1.-)
74
CYB5B CYB5M OMB5Cytochrome b5 type B (Cytochrome b5 outer mitochondrial membrane isoform)
76
CYB5R1 NQO3A2 UNQ3049/PRO9865NADH-cytochrome b5 reductase 1 (b5R.1) (EC 1.6.2.2) (NAD(P)H:quinone oxidoreductase type 3 polypeptide A2) (Humb5R2)
78
CYB5R2NADH-cytochrome b5 reductase 2 (b5R.2) (EC 1.6.2.2)
80
CYB5R3 DIA1NADH-cytochrome b5 reductase 3 (Cytochrome b5 reductase) (B5R) (EC 1.6.2.2) (Diaphorase-1) [Cleaved into: NADH-cytochrome b5 reductase 3 membrane-bound form; NADH-cytochrome b5 reductase 3 soluble form]
81
CYB5R4 NCB5ORCytochrome b5 reductase 4 (EC 1.6.2.2) (Flavohemoprotein b5/b5R) (b5+b5R) (cb5/cb5R) (N-terminal cytochrome b5 and cytochrome b5 oxidoreductase domain-containing protein)
82
CYB5RLNADH-cytochrome b5 reductase-like (EC 1.6.2.2)
83
CYBACytochrome b-245 light chain (p22 phagocyte B-cytochrome) (Neutrophil cytochrome b 22 kDa polypeptide) (p22-phox) (p22phox) (Cytochrome b(558) alpha chain) (Cytochrome b558 subunit alpha) (Superoxide-generating NADPH oxidase light chain subunit)
84
CYBB NOX2Cytochrome b-245 heavy chain (EC 1.-.-.-) (p22 phagocyte B-cytochrome) (Neutrophil cytochrome b 91 kDa polypeptide) (Heme-binding membrane glycoprotein gp91phox) (CGD91-phox) (gp91-phox) (gp91-1) (Cytochrome b(558) subunit beta) (Cytochrome b558 subunit beta) (Superoxide-generating NADPH oxidase heavy chain subunit) (NADPH oxidase 2)
85
CYP1A1Cytochrome P450 1A1 (EC 1.14.14.1) (CYPIA1) (Cytochrome P450-P1) (Cytochrome P450 form 6) (Cytochrome P450-C)
86
CYP1A2Cytochrome P450 1A2 (EC 1.14.14.1) (CYPIA2) (Cytochrome P450-P3) (Cytochrome P(3)450) (Cytochrome P450 4)
87
CYP1B1Cytochrome P450 1B1 (EC 1.14.14.1) (CYPIB1)
88
CYP24A1 CYP241,25-dihydroxyvitamin D(3) 24-hydroxylase, mitochondrial (Vitamin D(3) 24-hydroxylase) (24-OHase) (EC 1.14.13.n4) (Cytochrome P450 24A1) (Cytochrome P450-CC24)
89
CYP27A1 CYP27Sterol 26-hydroxylase, mitochondrial (EC 1.14.13.15) (Cytochrome P450 27) (Cytochrome P-450C27/25) (Sterol 27-hydroxylase) (Vitamin D(3) 25-hydroxylase) (5-beta-cholestane-3-alpha,7-alpha,12-alpha-triol 27-hydroxylase)
90
CYP27B1 CYP1ALPHA CYP27B25-hydroxyvitamin D-1 alpha hydroxylase, mitochondrial (EC 1.14.13.13) (Cytochrome P450 subfamily XXVIIB polypeptide 1) (Cytochrome p450 27B1) (Calcidiol 1-monooxygenase) (25-OHD-1 alpha-hydroxylase) (25-hydroxyvitamin D(3) 1-alpha-hydroxylase) (VD3 1A hydroxylase) (Cytochrome P450C1 alpha) (Cytochrome P450VD1-alpha)
92
CYP2A7Cytochrome P450 2A7 (EC 1.14.14.1) (CYPIIA7) (Cytochrome P450 IIA4)
93
CYP2B6Cytochrome P450 2B6 (EC 1.14.14.1) (CYPIIB6) (Cytochrome P450 IIB1)
95
CYP2C19Cytochrome P450 2C19 ((R)-limonene 6-monooxygenase) (EC 1.14.13.80) ((S)-limonene 6-monooxygenase) (EC 1.14.13.48) ((S)-limonene 7-monooxygenase) (EC 1.14.13.49) (CYPIIC19) (Cytochrome P450-11A) (Mephenytoin 4-hydroxylase) (CYPIIC17) (Cytochrome P450-254C)
97
CYP2C8Cytochrome P450 2C8 (EC 1.14.14.1) (CYPIIC8) (Cytochrome P450 form 1) (Cytochrome P450 MP-12) (Cytochrome P450 MP-20) (Cytochrome P450 IIC2) (S-mephenytoin 4-hydroxylase)
99
CYP2C9 CYP2C10Cytochrome P450 2C9 ((R)-limonene 6-monooxygenase) (EC 1.14.13.80) ((S)-limonene 6-monooxygenase) (EC 1.14.13.48) ((S)-limonene 7-monooxygenase) (EC 1.14.13.49) (CYPIIC9) (Cytochrome P450 PB-1) (Cytochrome P450 MP-4) (Cytochrome P450 MP-8) (S-mephenytoin 4-hydroxylase) (Cytochrome P-450MP)
101
CYP2E1 CYP2ECytochrome P450 2E1 (EC 1.14.13.-) (CYPIIE1) (4-nitrophenol 2-hydroxylase) (EC 1.14.13.n7) (Cytochrome P450-J)
103
CYP2J2Cytochrome P450 2J2 (EC 1.14.14.1) (CYPIIJ2) (Arachidonic acid epoxygenase)
104
CYP2R1Vitamin D 25-hydroxylase (EC 1.14.13.15) (Cytochrome P450 2R1)
106
CYP39A124-hydroxycholesterol 7-alpha-hydroxylase (Oxysterol 7-alpha-hydroxylase) (EC 1.14.13.99) (Cytochrome P450 39A1) (hCYP39A1)
107
CYP3A4 CYP3A3Cytochrome P450 3A4 (Quinine 3-monooxygenase) (EC 1.14.13.67) (CYPIIIA4) (Nifedipine oxidase) (Cytochrome P450 3A3) (CYPIIIA3) (Cytochrome P450 HLp) (Taurochenodeoxycholate 6-alpha-hydroxylase) (EC 1.14.13.97) (Cytochrome P450 NF-25) (Cytochrome P450-PCN1) (Albendazole monooxygenase) (EC 1.14.13.32) (Albendazole sulfoxidase)
109
CYP3A5Cytochrome P450 3A5 (EC 1.14.14.1) (CYPIIIA5) (Cytochrome P450-PCN3) (Cytochrome P450 HLp2)
111
CYP3A7Cytochrome P450 3A7 (EC 1.14.14.1) (CYPIIIA7) (Cytochrome P450-HFLA)
113
CYP46A1 CYP46Cholesterol 24-hydroxylase (CH24H) (EC 1.14.13.98) (Cytochrome P450 46A1)
115
CYP4B1Cytochrome P450 4B1 (EC 1.14.14.1) (CYPIVB1) (Cytochrome P450-HP)
116
CYP4F2Leukotriene-B(4) omega-hydroxylase 1 (EC 1.14.13.30) (Cytochrome P450 4F2) (CYPIVF2) (Leukotriene-B(4) 20-monooxygenase 1) (Cytochrome P450-LTB-omega)
117
CYP4F3 LTB4HLeukotriene-B(4) omega-hydroxylase 2 (EC 1.14.13.30) (Cytochrome P450 4F3) (CYPIVF3) (Leukotriene-B(4) 20-monooxygenase 2) (Cytochrome P450-LTB-omega)
119
CYP51A1 CYP51Lanosterol 14-alpha demethylase (LDM) (EC 1.14.13.70) (Cytochrome P450 51A1) (CYPLI) (Cytochrome P450LI) (Sterol 14-alpha demethylase) (Cytochrome P450-14DM) (Cytochrome P45014DM)
120
CYP7A1 CYP7Cholesterol 7-alpha-monooxygenase (EC 1.14.13.17) (Cytochrome P450 7A1) (CYPVII) (Cholesterol 7-alpha-hydroxylase)
122
CYP7B125-hydroxycholesterol 7-alpha-hydroxylase (Oxysterol 7-alpha-hydroxylase) (EC 1.14.13.100) (Cytochrome P450 7B1)
124
CYP8B1 CYP127-alpha-hydroxycholest-4-en-3-one 12-alpha-hydroxylase (EC 1.14.13.95) (Cytochrome P450 8B1) (CYPVIIIB1) (7-alpha-hydroxy-4-cholesten-3-one 12-alpha-hydroxylase) (Sterol 12-alpha-hydroxylase)
126
DCXRL-xylulose reductase (XR) (EC 1.1.1.10) (Dicarbonyl/L-xylulose reductase) (Kidney dicarbonyl reductase) (kiDCR) (Carbonyl reductase II) (Sperm surface protein P34H)
127
DECR1 DECR2,4-dienoyl-CoA reductase, mitochondrial (EC 1.3.1.34) (2,4-dienoyl-CoA reductase [NADPH]) (4-enoyl-CoA reductase [NADPH])
129
DECR2 PDCRPeroxisomal 2,4-dienoyl-CoA reductase (pDCR) (EC 1.3.1.34) (2,4-dienoyl-CoA reductase 2)
131
DHCR7 D7SR7-dehydrocholesterol reductase (7-DHC reductase) (EC 1.3.1.21) (Sterol Delta(7)-reductase) (Putative sterol reductase SR-2)
132
DHDH 2DDTrans-1,2-dihydrobenzene-1,2-diol dehydrogenase (EC 1.3.1.20) (Dimeric dihydrodiol dehydrogenase) (D-xylose-NADP dehydrogenase) (EC 1.1.1.179) (D-xylose 1-dehydrogenase) (Hum2DD)