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1 | Pathway identifier | Pathway name | #Entities found | #Entities total | Entities ratio | Entities pValue | Entities FDR | #Reactions found | #Reactions total | Reactions ratio | Species identifier | Species name | Submitted entities found | Mapped entities | Found reaction identifiers | |||||||||||
2 | R-HSA-9840310 | Glycosphingolipid catabolism | 20 | 78 | 0.0050093121829041165 | 1.1102230246251565E-16 | 1.5543122344752192E-15 | 26 | 34 | 0.0022837184309511017 | 9606 | Homo sapiens | ARSA;ASAH1;ASAH2;GBA;GBA2;NEU2;SMPD3;GALC;NEU3;SMPD2;NEU4;SMPD4;GLB1;SMPD1;PSAP;NEU1;GLA;ENPP7 | R-HSA-9840470;R-HSA-1861788;R-HSA-1614362;R-HSA-1605723;R-HSA-1605724;R-HSA-1606288;R-HSA-9840795;R-HSA-1606807;R-HSA-1605591;R-HSA-1605768;R-HSA-1606602;R-HSA-9842115;R-HSA-9840334;R-HSA-1605632;R-HSA-2248891;R-HSA-1606273;R-HSA-1605624;R-HSA-9840949;R-HSA-1606583;R-HSA-1605736;R-HSA-1606312;R-HSA-9841189;R-HSA-1606564;R-HSA-1605797;R-HSA-1640164;R-HSA-9840488 | ||||||||||||
3 | R-HSA-1660662 | Glycosphingolipid metabolism | 25 | 138 | 0.008862629246676515 | 1.1102230246251565E-16 | 1.5543122344752192E-15 | 31 | 49 | 0.003291241268135411 | 9606 | Homo sapiens | ARSA;ASAH1;GAL3ST1;ASAH2;CERK;GBA;GBA2;NEU2;SMPD3;GALC;NEU3;SMPD2;UGT8;UGCG;NEU4;SMPD4;GLB1;SMPD1;PSAP;NEU1;B4GALT6;GLA;ENPP7 | R-HSA-1638104;R-HSA-9840470;R-HSA-1861788;R-HSA-1614362;R-HSA-1605723;R-HSA-1605724;R-HSA-9851347;R-HSA-1606288;R-HSA-9840795;R-HSA-1606807;R-HSA-1605591;R-HSA-1605768;R-HSA-1606602;R-HSA-9842115;R-HSA-9840334;R-HSA-1605632;R-HSA-2248891;R-HSA-1606273;R-HSA-1605624;R-HSA-9840949;R-HSA-1638845;R-HSA-6785933;R-HSA-1606583;R-HSA-1605736;R-HSA-1606312;R-HSA-9841189;R-HSA-1606564;R-HSA-9844587;R-HSA-1605797;R-HSA-1640164;R-HSA-9840488 | ||||||||||||
4 | R-HSA-428157 | Sphingolipid metabolism | 50 | 221 | 0.014193051184894997 | 1.1102230246251565E-16 | 1.5543122344752192E-15 | 48 | 80 | 0.0053734551316496505 | 9606 | Homo sapiens | ASAH1;GAL3ST1;ASAH2;SGMS1;CERK;GBA;SGMS2;GBA2;NEU2;SMPD3;NEU3;UGT8;UGCG;SMPD2;SGPL1;NEU4;SMPD4;SPTLC1;SPTLC2;SPTLC3;SMPD1;PSAP;NEU1;KDSR;ENPP7;CERS3;CERS4;ARSA;CERS5;CERS6;SPHK2;SPHK1;SGPP2;SGPP1;ACER2;GALC;ACER1;GLB1;ACER3;DEGS1;DEGS2;PLPP3;B4GALT6;GLA;PLPP2;CERS1;PLPP1;CERS2 | R-HSA-1861788;R-HSA-1638104;R-HSA-9840470;R-HSA-428231;R-HSA-1614362;R-HSA-1605723;R-HSA-1605724;R-HSA-9851347;R-HSA-1606288;R-HSA-9840795;R-HSA-428681;R-HSA-1606807;R-HSA-1605591;R-HSA-1605768;R-HSA-1606602;R-HSA-428690;R-HSA-9842115;R-HSA-1605632;R-HSA-9840334;R-HSA-2248891;R-HSA-1606273;R-HSA-428127;R-HSA-429786;R-HSA-428123;R-HSA-428696;R-HSA-9695949;R-HSA-428185;R-HSA-429798;R-HSA-1605624;R-HSA-428262;R-HSA-428260;R-HSA-9840949;R-HSA-1638845;R-HSA-428259;R-HSA-6785933;R-HSA-428205;R-HSA-1606583;R-HSA-1606312;R-HSA-1605736;R-HSA-9841189;R-HSA-428273;R-HSA-1606564;R-HSA-1605797;R-HSA-9844587;R-HSA-1640164;R-HSA-9695917;R-HSA-9840488;R-HSA-428664 | ||||||||||||
5 | R-HSA-1660661 | Sphingolipid de novo biosynthesis | 16 | 68 | 0.004367092672275383 | 1.1102230246251565E-16 | 1.5543122344752192E-15 | 10 | 21 | 0.0014105319720580333 | 9606 | Homo sapiens | CERS3;CERS4;CERS5;CERS6;SGMS1;SPHK2;SPHK1;SGMS2;SPTLC1;SPTLC2;SPTLC3;DEGS1;KDSR;DEGS2;CERS1;CERS2 | R-HSA-429798;R-HSA-428260;R-HSA-428259;R-HSA-428273;R-HSA-428127;R-HSA-429786;R-HSA-428123;R-HSA-9695949;R-HSA-9695917;R-HSA-428185 | ||||||||||||
6 | R-HSA-556833 | Metabolism of lipids | 50 | 1504 | 0.09658981439856143 | 1.1102230246251565E-16 | 1.5543122344752192E-15 | 48 | 980 | 0.06582482536270823 | 9606 | Homo sapiens | ASAH1;GAL3ST1;ASAH2;SGMS1;CERK;GBA;SGMS2;GBA2;NEU2;SMPD3;NEU3;UGT8;UGCG;SMPD2;SGPL1;NEU4;SMPD4;SPTLC1;SPTLC2;SPTLC3;SMPD1;PSAP;NEU1;KDSR;ENPP7;CERS3;CERS4;ARSA;CERS5;CERS6;SPHK2;SPHK1;SGPP2;SGPP1;ACER2;GALC;ACER1;GLB1;ACER3;DEGS1;DEGS2;PLPP3;B4GALT6;GLA;PLPP2;CERS1;PLPP1;CERS2 | R-HSA-1861788;R-HSA-1638104;R-HSA-9840470;R-HSA-428231;R-HSA-1614362;R-HSA-1605723;R-HSA-1605724;R-HSA-9851347;R-HSA-1606288;R-HSA-9840795;R-HSA-428681;R-HSA-1606807;R-HSA-1605591;R-HSA-1605768;R-HSA-1606602;R-HSA-428690;R-HSA-9842115;R-HSA-1605632;R-HSA-9840334;R-HSA-2248891;R-HSA-1606273;R-HSA-428127;R-HSA-429786;R-HSA-428123;R-HSA-428696;R-HSA-9695949;R-HSA-428185;R-HSA-429798;R-HSA-1605624;R-HSA-428262;R-HSA-428260;R-HSA-9840949;R-HSA-1638845;R-HSA-428259;R-HSA-6785933;R-HSA-428205;R-HSA-1606583;R-HSA-1606312;R-HSA-1605736;R-HSA-9841189;R-HSA-428273;R-HSA-1606564;R-HSA-1605797;R-HSA-9844587;R-HSA-1640164;R-HSA-9695917;R-HSA-9840488;R-HSA-428664 | ||||||||||||
7 | R-HSA-1430728 | Metabolism | 50 | 3717 | 0.23871299210070002 | 1.1102230246251565E-16 | 1.5543122344752192E-15 | 53 | 2309 | 0.15509134873723804 | 9606 | Homo sapiens | ASAH1;GAL3ST1;ASAH2;SGMS1;CERK;GBA;SGMS2;GBA2;NEU2;SMPD3;NEU3;UGT8;UGCG;SMPD2;SGPL1;NEU4;SMPD4;SPTLC1;SPTLC2;SPTLC3;SMPD1;PSAP;NEU1;KDSR;ENPP7;CERS3;CERS4;ARSA;CERS5;CERS6;SPHK2;SPHK1;SGPP2;SGPP1;ACER2;GALC;ACER1;GLB1;ACER3;DEGS1;DEGS2;PLPP3;B4GALT6;GLA;PLPP2;CERS1;PLPP1;CERS2 | R-HSA-1861788;R-HSA-1614362;R-HSA-1606288;R-HSA-9840795;R-HSA-428681;R-HSA-1606807;R-HSA-1605768;R-HSA-428690;R-HSA-1605632;R-HSA-2248891;R-HSA-1606273;R-HSA-428696;R-HSA-428185;R-HSA-9840949;R-HSA-1638845;R-HSA-2046265;R-HSA-428205;R-HSA-1606583;R-HSA-1606312;R-HSA-9841189;R-HSA-1606564;R-HSA-1605797;R-HSA-9695917;R-HSA-1638104;R-HSA-9840470;R-HSA-2090079;R-HSA-428231;R-HSA-1605723;R-HSA-1605724;R-HSA-9851347;R-HSA-2046298;R-HSA-1605591;R-HSA-1606602;R-HSA-9842115;R-HSA-9840334;R-HSA-428127;R-HSA-429786;R-HSA-428123;R-HSA-9695949;R-HSA-429798;R-HSA-1605624;R-HSA-428262;R-HSA-428260;R-HSA-428259;R-HSA-2025723;R-HSA-6785933;R-HSA-1605736;R-HSA-428273;R-HSA-1630306;R-HSA-9844587;R-HSA-1640164;R-HSA-9840488;R-HSA-428664 | ||||||||||||
8 | R-HSA-9845614 | Sphingolipid catabolism | 9 | 32 | 0.0020551024340119454 | 7.438494264988549E-15 | 8.926193117986259E-14 | 7 | 10 | 6.716818914562063E-4 | 9606 | Homo sapiens | ACER2;ACER1;SGPL1;ACER3;PLPP3;PLPP2;SGPP2;PLPP1;SGPP1 | R-HSA-428262;R-HSA-428231;R-HSA-428690;R-HSA-428205;R-HSA-428664;R-HSA-428696;R-HSA-428681 | ||||||||||||
9 | R-HSA-4085001 | Sialic acid metabolism | 5 | 67 | 0.00430287072121251 | 6.085628591834258E-6 | 6.694191451017684E-5 | 4 | 21 | 0.0014105319720580333 | 9606 | Homo sapiens | NEU2;NEU3;NEU4;GLB1;NEU1 | R-HSA-4084999;R-HSA-9638120;R-HSA-4085029;R-HSA-4084994 | ||||||||||||
10 | R-HSA-9840309 | Glycosphingolipid biosynthesis | 5 | 73 | 0.00468820242758975 | 9.183978022520023E-6 | 8.26558022026802E-5 | 5 | 15 | 0.0010075228371843096 | 9606 | Homo sapiens | UGT8;UGCG;GAL3ST1;CERK;B4GALT6 | R-HSA-1638104;R-HSA-1638845;R-HSA-9851347;R-HSA-6785933;R-HSA-9844587 | ||||||||||||
11 | R-HSA-5683826 | Surfactant metabolism | 4 | 52 | 0.0033395414552694113 | 4.8884732394616215E-5 | 3.910778591569297E-4 | 8 | 29 | 0.0019478774852229985 | 9606 | Homo sapiens | PSAP | R-HSA-5686359;R-HSA-5683879;R-HSA-5687284;R-HSA-5685296;R-HSA-5685649;R-HSA-5686286;R-HSA-5686335;R-HSA-5686301 | ||||||||||||
12 | R-HSA-1638074 | Keratan sulfate/keratin metabolism | 4 | 54 | 0.0034679853573951576 | 5.653132613891998E-5 | 4.5225060911135984E-4 | 4 | 16 | 0.0010746910263299302 | 9606 | Homo sapiens | GLB1;B4GALT6 | R-HSA-2046298;R-HSA-2025723;R-HSA-2046265;R-HSA-1630306 | ||||||||||||
13 | R-HSA-2022857 | Keratan sulfate degradation | 3 | 24 | 0.001541326825508959 | 1.1158792139298601E-4 | 7.811154497509021E-4 | 1 | 7 | 4.7017732401934446E-4 | 9606 | Homo sapiens | GLB1 | R-HSA-1630306 | ||||||||||||
14 | R-HSA-446219 | Synthesis of substrates in N-glycan biosythesis | 5 | 139 | 0.008926851197739387 | 1.9007614988375554E-4 | 0.0011404568993025332 | 4 | 49 | 0.003291241268135411 | 9606 | Homo sapiens | NEU2;NEU3;NEU4;GLB1;NEU1 | R-HSA-4084999;R-HSA-9638120;R-HSA-4085029;R-HSA-4084994 | ||||||||||||
15 | R-HSA-5626978 | TNFR1-mediated ceramide production | 2 | 6 | 3.8533170637723973E-4 | 2.5036015249002563E-4 | 0.0015021609149401538 | 1 | 3 | 2.015045674368619E-4 | 9606 | Homo sapiens | SMPD3;SMPD2 | R-HSA-5626981 | ||||||||||||
16 | R-HSA-446193 | Biosynthesis of the N-glycan precursor (dolichol lipid-linked oligosaccharide, LLO) and transfer to a nascent protein | 5 | 167 | 0.01072506582749984 | 4.3900466129265237E-4 | 0.0017716860300658333 | 4 | 63 | 0.0042315959161741 | 9606 | Homo sapiens | NEU2;NEU3;NEU4;GLB1;NEU1 | R-HSA-4084999;R-HSA-9638120;R-HSA-4085029;R-HSA-4084994 | ||||||||||||
17 | R-HSA-5688890 | Defective CSF2RA causes SMDP4 | 2 | 8 | 5.137756085029863E-4 | 4.429215075164583E-4 | 0.0017716860300658333 | 1 | 1 | 6.716818914562064E-5 | 9606 | Homo sapiens | PSAP | R-HSA-5688899 | ||||||||||||
18 | R-HSA-4341670 | Defective NEU1 causes sialidosis | 2 | 8 | 5.137756085029863E-4 | 4.429215075164583E-4 | 0.0017716860300658333 | 1 | 1 | 6.716818914562064E-5 | 9606 | Homo sapiens | GLB1;NEU1 | R-HSA-4341669 | ||||||||||||
19 | R-HSA-5688849 | Defective CSF2RB causes SMDP5 | 2 | 8 | 5.137756085029863E-4 | 4.429215075164583E-4 | 0.0017716860300658333 | 1 | 1 | 6.716818914562064E-5 | 9606 | Homo sapiens | PSAP | R-HSA-5688884 | ||||||||||||
20 | R-HSA-2024096 | HS-GAG degradation | 3 | 46 | 0.0029542097488921715 | 7.406341668411143E-4 | 0.002962536667364457 | 1 | 14 | 9.403546480386889E-4 | 9606 | Homo sapiens | GLB1 | R-HSA-2090079 | ||||||||||||
21 | R-HSA-5687613 | Diseases associated with surfactant metabolism | 2 | 16 | 0.0010275512170059727 | 0.001737537143336798 | 0.006950148573347192 | 3 | 7 | 4.7017732401934446E-4 | 9606 | Homo sapiens | PSAP | R-HSA-5688884;R-HSA-5688899;R-HSA-5687875 | ||||||||||||
22 | R-HSA-6798695 | Neutrophil degranulation | 7 | 478 | 0.030698092608053434 | 0.0021645371280454295 | 0.008658148512181718 | 6 | 10 | 6.716818914562063E-4 | 9606 | Homo sapiens | ARSA;ASAH1;GLB1;PSAP;NEU1;DEGS1;GLA | R-HSA-6799350;R-HSA-6798739;R-HSA-6800434;R-HSA-6798751;R-HSA-6798749;R-HSA-6798745 | ||||||||||||
23 | R-HSA-391160 | Signal regulatory protein family interactions | 2 | 18 | 0.0011559951191317192 | 0.002188410201991897 | 0.008753640807967589 | 1 | 10 | 6.716818914562063E-4 | 9606 | Homo sapiens | PSAP | R-HSA-391155 | ||||||||||||
24 | R-HSA-5687868 | Defective SFTPA2 causes IPF | 1 | 1 | 6.422195106287329E-5 | 0.003782046766639846 | 0.011346140299919538 | 1 | 1 | 6.716818914562064E-5 | 9606 | Homo sapiens | PSAP | R-HSA-5687875 | ||||||||||||
25 | R-HSA-1638091 | Heparan sulfate/heparin (HS-GAG) metabolism | 3 | 89 | 0.005715753644595723 | 0.004781709570826687 | 0.01434512871248006 | 1 | 33 | 0.002216550241805481 | 9606 | Homo sapiens | GLB1 | R-HSA-2090079 | ||||||||||||
26 | R-HSA-9857377 | Regulation of MITF-M-dependent genes involved in lysosome biogenesis and autophagy | 2 | 28 | 0.0017982146297604521 | 0.00516849788261764 | 0.01550549364785292 | 2 | 13 | 8.731864588930683E-4 | 9606 | Homo sapiens | ASAH1 | R-HSA-9859104;R-HSA-9859098 | ||||||||||||
27 | R-HSA-1630316 | Glycosaminoglycan metabolism | 4 | 183 | 0.011752617044505812 | 0.005194406043920963 | 0.015583218131762888 | 5 | 88 | 0.005910800644814616 | 9606 | Homo sapiens | GLB1;B4GALT6 | R-HSA-2090079;R-HSA-2046298;R-HSA-2025723;R-HSA-2046265;R-HSA-1630306 | ||||||||||||
28 | R-HSA-446203 | Asparagine N-linked glycosylation | 6 | 431 | 0.027679660908098386 | 0.005780942731446581 | 0.017342828194339743 | 5 | 144 | 0.00967221923696937 | 9606 | Homo sapiens | NEU2;NEU3;NEU4;GLB1;NEU1;B4GALT6 | R-HSA-975919;R-HSA-4084999;R-HSA-9638120;R-HSA-4085029;R-HSA-4084994 | ||||||||||||
29 | R-HSA-390471 | Association of TriC/CCT with target proteins during biosynthesis | 2 | 40 | 0.002568878042514932 | 0.010246192917022556 | 0.026711636941910477 | 2 | 2 | 1.3433637829124128E-4 | 9606 | Homo sapiens | SPHK1;GBA | R-HSA-390470;R-HSA-391266 | ||||||||||||
30 | R-HSA-5686938 | Regulation of TLR by endogenous ligand | 2 | 41 | 0.002633099993577805 | 0.010738944664687167 | 0.026711636941910477 | 2 | 13 | 8.731864588930683E-4 | 9606 | Homo sapiens | PSAP | R-HSA-5432852;R-HSA-5432814 | ||||||||||||
31 | R-HSA-3781860 | Diseases associated with N-glycosylation of proteins | 2 | 46 | 0.0029542097488921715 | 0.013355818470955239 | 0.026711636941910477 | 1 | 24 | 0.0016120365394948952 | 9606 | Homo sapiens | GLB1;NEU1 | R-HSA-4341669 | ||||||||||||
32 | R-HSA-2206308 | MPS IV - Morquio syndrome B | 1 | 4 | 2.5688780425149317E-4 | 0.015044018389521852 | 0.030088036779043703 | 2 | 2 | 1.3433637829124128E-4 | 9606 | Homo sapiens | GLB1 | R-HSA-9036061;R-HSA-2265534 | ||||||||||||
33 | R-HSA-75893 | TNF signaling | 2 | 64 | 0.004110204868023891 | 0.024757849958936595 | 0.04951569991787319 | 1 | 58 | 0.003895754970445997 | 9606 | Homo sapiens | SMPD3;SMPD2 | R-HSA-5626981 | ||||||||||||
34 | R-HSA-193681 | Ceramide signalling | 1 | 8 | 5.137756085029863E-4 | 0.029865493446926017 | 0.059730986893852034 | 2 | 2 | 1.3433637829124128E-4 | 9606 | Homo sapiens | SMPD2 | R-HSA-193706;R-HSA-193672 | ||||||||||||
35 | R-HSA-390466 | Chaperonin-mediated protein folding | 2 | 96 | 0.006165307302035836 | 0.051605978860976065 | 0.09422468808309448 | 2 | 19 | 0.001276195593766792 | 9606 | Homo sapiens | SPHK1;GBA | R-HSA-390470;R-HSA-391266 | ||||||||||||
36 | R-HSA-392499 | Metabolism of proteins | 14 | 2345 | 0.15060047524243786 | 0.052587790340352436 | 0.09422468808309448 | 18 | 846 | 0.05682428801719506 | 9606 | Homo sapiens | NEU2;ARSA;NEU3;NEU4;GLB1;SPHK1;PSAP;NEU1;GBA;B4GALT6;GLA | R-HSA-5686359;R-HSA-975919;R-HSA-5687284;R-HSA-1614362;R-HSA-390470;R-HSA-5685296;R-HSA-391266;R-HSA-5685649;R-HSA-1964501;R-HSA-5686335;R-HSA-5686301;R-HSA-5683879;R-HSA-5686286;R-HSA-4084999;R-HSA-9638120;R-HSA-4085029;R-HSA-4084994;R-HSA-5693001 | ||||||||||||
37 | R-HSA-391251 | Protein folding | 2 | 102 | 0.006550639008413075 | 0.05743372877965702 | 0.09422468808309448 | 2 | 28 | 0.0018807092960773778 | 9606 | Homo sapiens | SPHK1;GBA | R-HSA-390470;R-HSA-391266 | ||||||||||||
38 | R-HSA-168249 | Innate Immune System | 9 | 1345 | 0.08637852417956457 | 0.0655417287663097 | 0.09422468808309448 | 10 | 738 | 0.04957012358946803 | 9606 | Homo sapiens | ARSA;ASAH1;GLB1;PSAP;NEU1;DEGS1;GLA | R-HSA-6799350;R-HSA-6798739;R-HSA-6800434;R-HSA-168951;R-HSA-5432852;R-HSA-6798751;R-HSA-6798749;R-HSA-166041;R-HSA-5432814;R-HSA-6798745 | ||||||||||||
39 | R-HSA-1663150 | The activation of arylsulfatases | 1 | 18 | 0.0011559951191317192 | 0.06596667733202155 | 0.09422468808309448 | 1 | 2 | 1.3433637829124128E-4 | 9606 | Homo sapiens | ARSA | R-HSA-1614362 | ||||||||||||
40 | R-HSA-975577 | N-Glycan antennae elongation | 1 | 20 | 0.001284439021257466 | 0.07302678914243288 | 0.09422468808309448 | 1 | 6 | 4.030091348737238E-4 | 9606 | Homo sapiens | B4GALT6 | R-HSA-975919 | ||||||||||||
41 | R-HSA-5668914 | Diseases of metabolism | 4 | 424 | 0.027230107250658275 | 0.07703851856042776 | 0.09422468808309448 | 6 | 195 | 0.013097796883396023 | 9606 | Homo sapiens | GLB1;PSAP;NEU1 | R-HSA-5688884;R-HSA-9036061;R-HSA-5688899;R-HSA-5687875;R-HSA-4341669;R-HSA-2265534 | ||||||||||||
42 | R-HSA-9856651 | MITF-M-dependent gene expression | 2 | 131 | 0.008413075589236402 | 0.08845800802776527 | 0.09422468808309448 | 2 | 76 | 0.005104782375067168 | 9606 | Homo sapiens | ASAH1 | R-HSA-9859104;R-HSA-9859098 | ||||||||||||
43 | R-HSA-9609523 | Insertion of tail-anchored proteins into the endoplasmic reticulum membrane | 1 | 25 | 0.0016055487765718323 | 0.09044835985285693 | 0.09422468808309448 | 5 | 7 | 4.7017732401934446E-4 | 9606 | Homo sapiens | ARSA | R-HSA-9609860;R-HSA-9610442;R-HSA-9609899;R-HSA-9617596;R-HSA-9609917 | ||||||||||||
44 | R-HSA-71387 | Metabolism of carbohydrates | 4 | 453 | 0.0290925438314816 | 0.09277210222333832 | 0.09422468808309448 | 5 | 232 | 0.015583019881783988 | 9606 | Homo sapiens | GLB1;B4GALT6 | R-HSA-2090079;R-HSA-2046298;R-HSA-2025723;R-HSA-2046265;R-HSA-1630306 | ||||||||||||
45 | R-HSA-168179 | Toll Like Receptor TLR1:TLR2 Cascade | 2 | 136 | 0.008734185344550767 | 0.09422468808309448 | 0.09422468808309448 | 1 | 78 | 0.00523911875335841 | 9606 | Homo sapiens | PSAP | R-HSA-168951 | ||||||||||||
46 | R-HSA-181438 | Toll Like Receptor 2 (TLR2) Cascade | 2 | 136 | 0.008734185344550767 | 0.09422468808309448 | 0.09422468808309448 | 1 | 80 | 0.0053734551316496505 | 9606 | Homo sapiens | PSAP | R-HSA-168951 | ||||||||||||
47 | R-HSA-5218921 | VEGFR2 mediated cell proliferation | 1 | 31 | 0.001990880482949072 | 0.11092975448932363 | 0.11092975448932363 | 2 | 12 | 8.060182697474476E-4 | 9606 | Homo sapiens | SPHK1 | R-HSA-5218845;R-HSA-5218823 | ||||||||||||
48 | R-HSA-2206281 | Mucopolysaccharidoses | 1 | 36 | 0.0023119902382634384 | 0.12765069298244947 | 0.12765069298244947 | 2 | 22 | 0.001477700161203654 | 9606 | Homo sapiens | GLB1 | R-HSA-9036061;R-HSA-2265534 | ||||||||||||
49 | R-HSA-1500931 | Cell-Cell communication | 2 | 165 | 0.010596621925374092 | 0.12959255910502998 | 0.12959255910502998 | 1 | 93 | 0.006246641590542719 | 9606 | Homo sapiens | PSAP | R-HSA-391155 | ||||||||||||
50 | R-HSA-166016 | Toll Like Receptor 4 (TLR4) Cascade | 2 | 166 | 0.010660843876436966 | 0.13086291136414696 | 0.13086291136414696 | 1 | 113 | 0.007590005373455132 | 9606 | Homo sapiens | PSAP | R-HSA-166041 | ||||||||||||
51 | R-HSA-2022854 | Keratan sulfate biosynthesis | 1 | 37 | 0.002376212189326312 | 0.13095759014130526 | 0.13095759014130526 | 3 | 9 | 6.045137023105857E-4 | 9606 | Homo sapiens | B4GALT6 | R-HSA-2046298;R-HSA-2025723;R-HSA-2046265 | ||||||||||||
52 | R-HSA-9730414 | MITF-M-regulated melanocyte development | 2 | 167 | 0.01072506582749984 | 0.13213621939127396 | 0.13213621939127396 | 2 | 94 | 0.00631380977968834 | 9606 | Homo sapiens | ASAH1 | R-HSA-9859104;R-HSA-9859098 | ||||||||||||
53 | R-HSA-73887 | Death Receptor Signaling | 2 | 172 | 0.011046175582814207 | 0.1385457233072298 | 0.1385457233072298 | 3 | 119 | 0.007993014508328856 | 9606 | Homo sapiens | SMPD3;SMPD2 | R-HSA-5626981;R-HSA-193706;R-HSA-193672 | ||||||||||||
54 | R-HSA-975576 | N-glycan antennae elongation in the medial/trans-Golgi | 1 | 47 | 0.0030184316999550447 | 0.16335613158750173 | 0.16335613158750173 | 1 | 14 | 9.403546480386889E-4 | 9606 | Homo sapiens | B4GALT6 | R-HSA-975919 | ||||||||||||
55 | R-HSA-3781865 | Diseases of glycosylation | 2 | 202 | 0.012972834114700404 | 0.17827324426695823 | 0.17827324426695823 | 1 | 77 | 0.005171950564212789 | 9606 | Homo sapiens | GLB1;NEU1 | R-HSA-4341669 | ||||||||||||
56 | R-HSA-168898 | Toll-like Receptor Cascades | 2 | 207 | 0.013293943870014771 | 0.18506578082812175 | 0.18506578082812175 | 4 | 211 | 0.014172487909725954 | 9606 | Homo sapiens | PSAP | R-HSA-168951;R-HSA-5432852;R-HSA-166041;R-HSA-5432814 | ||||||||||||
57 | R-HSA-913709 | O-linked glycosylation of mucins | 1 | 73 | 0.00468820242758975 | 0.24213830054708008 | 0.24213830054708008 | 1 | 16 | 0.0010746910263299302 | 9606 | Homo sapiens | B4GALT6 | R-HSA-1964501 | ||||||||||||
58 | R-HSA-5663084 | Diseases of carbohydrate metabolism | 1 | 81 | 0.005201978036092737 | 0.26487723786272055 | 0.26487723786272055 | 2 | 44 | 0.002955400322407308 | 9606 | Homo sapiens | GLB1 | R-HSA-9036061;R-HSA-2265534 | ||||||||||||
59 | R-HSA-9833482 | PKR-mediated signaling | 1 | 88 | 0.00565153169353285 | 0.2842226753262109 | 0.2842226753262109 | 4 | 40 | 0.0026867275658248252 | 9606 | Homo sapiens | SPHK1 | R-HSA-9836606;R-HSA-9836621;R-HSA-9833723;R-HSA-9836617 | ||||||||||||
60 | R-HSA-977225 | Amyloid fiber formation | 1 | 89 | 0.005715753644595723 | 0.2869451360767179 | 0.2869451360767179 | 1 | 33 | 0.002216550241805481 | 9606 | Homo sapiens | GLA | R-HSA-5693001 | ||||||||||||
61 | R-HSA-163841 | Gamma carboxylation, hypusinylation, hydroxylation, and arylsulfatase activation | 1 | 95 | 0.0061010853509729625 | 0.3030674245316093 | 0.3030674245316093 | 1 | 50 | 0.0033584094572810318 | 9606 | Homo sapiens | ARSA | R-HSA-1614362 | ||||||||||||
62 | R-HSA-193704 | p75 NTR receptor-mediated signalling | 1 | 110 | 0.007064414616916062 | 0.3418218624858248 | 0.3418218624858248 | 2 | 50 | 0.0033584094572810318 | 9606 | Homo sapiens | SMPD2 | R-HSA-193706;R-HSA-193672 | ||||||||||||
63 | R-HSA-9009391 | Extra-nuclear estrogen signaling | 1 | 111 | 0.007128636567978935 | 0.34432880006422917 | 0.34432880006422917 | 1 | 39 | 0.002619559376679205 | 9606 | Homo sapiens | SPHK1 | R-HSA-9625814 | ||||||||||||
64 | R-HSA-4420097 | VEGFA-VEGFR2 Pathway | 1 | 129 | 0.008284631687110654 | 0.3878814208071323 | 0.3878814208071323 | 2 | 79 | 0.00530628694250403 | 9606 | Homo sapiens | SPHK1 | R-HSA-5218845;R-HSA-5218823 | ||||||||||||
65 | R-HSA-5173105 | O-linked glycosylation | 1 | 133 | 0.008541519491362148 | 0.3971664956475355 | 0.3971664956475355 | 1 | 27 | 0.0018135411069317572 | 9606 | Homo sapiens | B4GALT6 | R-HSA-1964501 | ||||||||||||
66 | R-HSA-194138 | Signaling by VEGF | 1 | 140 | 0.008991073148802261 | 0.41308335412089103 | 0.41308335412089103 | 2 | 86 | 0.005776464266523375 | 9606 | Homo sapiens | SPHK1 | R-HSA-5218845;R-HSA-5218823 | ||||||||||||
67 | R-HSA-114608 | Platelet degranulation | 1 | 141 | 0.009055295099865133 | 0.415323201469619 | 0.415323201469619 | 1 | 11 | 7.38850080601827E-4 | 9606 | Homo sapiens | PSAP | R-HSA-351341 | ||||||||||||
68 | R-HSA-76005 | Response to elevated platelet cytosolic Ca2+ | 1 | 148 | 0.009504848757305248 | 0.4307685600438783 | 0.4307685600438783 | 1 | 14 | 9.403546480386889E-4 | 9606 | Homo sapiens | PSAP | R-HSA-351341 | ||||||||||||
69 | R-HSA-597592 | Post-translational protein modification | 7 | 1653 | 0.10615888510692954 | 0.43818763909149905 | 0.43818763909149905 | 7 | 553 | 0.037144008597528214 | 9606 | Homo sapiens | NEU2;ARSA;NEU3;NEU4;GLB1;NEU1;B4GALT6 | R-HSA-975919;R-HSA-1614362;R-HSA-1964501;R-HSA-4084999;R-HSA-9638120;R-HSA-4085029;R-HSA-4084994 | ||||||||||||
70 | R-HSA-9609507 | Protein localization | 1 | 171 | 0.010981953631751333 | 0.47874677870331717 | 0.47874677870331717 | 5 | 53 | 0.0035599140247178935 | 9606 | Homo sapiens | ARSA | R-HSA-9609860;R-HSA-9610442;R-HSA-9609899;R-HSA-9617596;R-HSA-9609917 | ||||||||||||
71 | R-HSA-1169410 | Antiviral mechanism by IFN-stimulated genes | 1 | 172 | 0.011046175582814207 | 0.4807400318318401 | 0.4807400318318401 | 4 | 71 | 0.004768941429339065 | 9606 | Homo sapiens | SPHK1 | R-HSA-9836606;R-HSA-9836621;R-HSA-9833723;R-HSA-9836617 | ||||||||||||
72 | R-HSA-375276 | Peptide ligand-binding receptors | 1 | 203 | 0.013037056065763278 | 0.5389479239756565 | 0.5389479239756565 | 2 | 83 | 0.005574959699086513 | 9606 | Homo sapiens | PSAP | R-HSA-5336182;R-HSA-5336184 | ||||||||||||
73 | R-HSA-168256 | Immune System | 10 | 2663 | 0.17102305568043158 | 0.5661886382747718 | 0.5661886382747718 | 14 | 1717 | 0.11532778076303063 | 9606 | Homo sapiens | ARSA;ASAH1;GLB1;SPHK1;PSAP;NEU1;DEGS1;GLA | R-HSA-5432852;R-HSA-9836606;R-HSA-9833723;R-HSA-6799350;R-HSA-6798739;R-HSA-6800434;R-HSA-168951;R-HSA-6798751;R-HSA-6798749;R-HSA-9836621;R-HSA-166041;R-HSA-5432814;R-HSA-6798745;R-HSA-9836617 | ||||||||||||
74 | R-HSA-948021 | Transport to the Golgi and subsequent modification | 1 | 220 | 0.014128829233832125 | 0.5680933882988054 | 0.5680933882988054 | 1 | 60 | 0.004030091348737238 | 9606 | Homo sapiens | B4GALT6 | R-HSA-975919 | ||||||||||||
75 | R-HSA-8939211 | ESR-mediated signaling | 1 | 256 | 0.016440819472095563 | 0.6239641163469387 | 0.6239641163469387 | 1 | 114 | 0.007657173562600752 | 9606 | Homo sapiens | SPHK1 | R-HSA-9625814 | ||||||||||||
76 | R-HSA-76002 | Platelet activation, signaling and aggregation | 1 | 293 | 0.018817031661421874 | 0.6739756345183306 | 0.6739756345183306 | 1 | 119 | 0.007993014508328856 | 9606 | Homo sapiens | PSAP | R-HSA-351341 | ||||||||||||
77 | R-HSA-9006931 | Signaling by Nuclear Receptors | 1 | 388 | 0.024918117012394835 | 0.7743558117408005 | 0.7743558117408005 | 1 | 196 | 0.013164965072541644 | 9606 | Homo sapiens | SPHK1 | R-HSA-9625814 | ||||||||||||
78 | R-HSA-913531 | Interferon Signaling | 1 | 397 | 0.025496114571960698 | 0.78211319706887 | 0.78211319706887 | 4 | 119 | 0.007993014508328856 | 9606 | Homo sapiens | SPHK1 | R-HSA-9836606;R-HSA-9836621;R-HSA-9833723;R-HSA-9836617 | ||||||||||||
79 | R-HSA-373076 | Class A/1 (Rhodopsin-like receptors) | 1 | 414 | 0.026587887740029542 | 0.7960573732624451 | 0.7960573732624451 | 2 | 185 | 0.012426114991939817 | 9606 | Homo sapiens | PSAP | R-HSA-5336182;R-HSA-5336184 | ||||||||||||
80 | R-HSA-418594 | G alpha (i) signalling events | 1 | 426 | 0.02735855115278402 | 0.8053682869949528 | 0.8053682869949528 | 3 | 74 | 0.004970445996775927 | 9606 | Homo sapiens | PSAP | R-HSA-749454;R-HSA-749456;R-HSA-380073 | ||||||||||||
81 | R-HSA-500792 | GPCR ligand binding | 1 | 609 | 0.03911116819728983 | 0.9050017518554582 | 0.9050017518554582 | 2 | 217 | 0.014575497044599678 | 9606 | Homo sapiens | PSAP | R-HSA-5336182;R-HSA-5336184 | ||||||||||||
82 | R-HSA-9006934 | Signaling by Receptor Tyrosine Kinases | 1 | 634 | 0.040716716973861665 | 0.9139272455451678 | 0.9139272455451678 | 2 | 759 | 0.05098065556152606 | 9606 | Homo sapiens | SPHK1 | R-HSA-5218845;R-HSA-5218823 | ||||||||||||
83 | R-HSA-388396 | GPCR downstream signalling | 1 | 795 | 0.051056451094984266 | 0.9545867810846331 | 0.9545867810846331 | 3 | 175 | 0.011754433100483611 | 9606 | Homo sapiens | PSAP | R-HSA-749454;R-HSA-749456;R-HSA-380073 | ||||||||||||
84 | R-HSA-109582 | Hemostasis | 1 | 804 | 0.05163444865455012 | 0.9561902837360824 | 0.9561902837360824 | 1 | 342 | 0.02297152068780226 | 9606 | Homo sapiens | PSAP | R-HSA-351341 | ||||||||||||
85 | R-HSA-372790 | Signaling by GPCR | 1 | 876 | 0.056258429131077 | 0.9671653753011438 | 0.9671653753011438 | 5 | 392 | 0.026329930145083287 | 9606 | Homo sapiens | PSAP | R-HSA-749454;R-HSA-5336182;R-HSA-5336184;R-HSA-749456;R-HSA-380073 | ||||||||||||
86 | R-HSA-1280215 | Cytokine Signaling in Immune system | 1 | 1099 | 0.07057992421809775 | 0.9866797952745746 | 0.9866797952745746 | 4 | 785 | 0.052727028479312196 | 9606 | Homo sapiens | SPHK1 | R-HSA-9836606;R-HSA-9836621;R-HSA-9833723;R-HSA-9836617 | ||||||||||||
87 | R-HSA-1266738 | Developmental Biology | 2 | 1716 | 0.11020486802389057 | 0.9915359831394613 | 0.9915359831394613 | 2 | 889 | 0.05971252015045674 | 9606 | Homo sapiens | ASAH1 | R-HSA-9859104;R-HSA-9859098 | ||||||||||||
88 | R-HSA-1643685 | Disease | 4 | 2639 | 0.1694817288549226 | 0.9937110903475826 | 0.9937110903475826 | 6 | 1932 | 0.12976894142933906 | 9606 | Homo sapiens | GLB1;PSAP;NEU1 | R-HSA-5688884;R-HSA-9036061;R-HSA-5688899;R-HSA-5687875;R-HSA-4341669;R-HSA-2265534 | ||||||||||||
89 | R-HSA-162582 | Signal Transduction | 4 | 3038 | 0.19510628732900906 | 0.9984109195683395 | 0.9984109195683395 | 11 | 2549 | 0.171211714132187 | 9606 | Homo sapiens | SMPD3;SMPD2;SPHK1;PSAP | R-HSA-5626981;R-HSA-5218845;R-HSA-9625814;R-HSA-749454;R-HSA-5336182;R-HSA-5218823;R-HSA-193706;R-HSA-5336184;R-HSA-193672;R-HSA-749456;R-HSA-380073 | ||||||||||||
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