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Disease/definitionsAgingClinicalAnimal modelsMiscellaneous
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OrganIndicationSub-indication(s)Preclinical (animal) assaysHuman diagnostic measurementsEtiological hypothesis and acceptanceReferences used for columns D-FIncidence at age 25 (M/F)Incidence at age 50 (M/F)Incidence at age 75 (M/F)References used for columns H-JAging biology strongly implicatedAging biology weakly implicatedReferences used for columns L+MPatient population (US, 2022 unless noted)References for column SPrognosisCurrent Standard of Care TreatmentsClinical endpointsReferences for columns Q-STotal trial duration (months)*Trial enrollment (# people): Q1, Q2, Q3
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Phase 1Phase 2Phase 3Phase 1Phase 2Phase 3
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Q1Q2Q3Q1Q2Q3Q1Q2Q3Q1Q2Q3Q1Q2Q3Q1Q2Q3Current Clinical Pipeline (link)How well do mice model?Species that spontaneously get diseaseSpecies with human-like anatomy + physiologyNotes on model access/logisticsReferences for columns AN-AQExisting political lobbying strength for this diseaseExisting umbrella organization political lobbying strengthDisease costs/market (US)References for AU
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BrainAlzheimer'sFamilial AD (early onset), late onset AD, mixed dementiaNeuropsychological testing; imaging (PET, CT, MRI, multiphoton); biomarkers in CSF and blood; histologyPlaque formation; cognitive function; behavioral functionDominant hypothesis (amyloid beta) strongly supported by human genetics but recently under attack due to failure of treatments - i) accumulation of amyloid β (Aβ)
plaques (ii) accumulation of hypophosphorylated tau protein in the form of intracellular
neurofibrillary tangles (NFT) (iii) sustained inflammation and (iv) cerebrovascular damage and dysfunction
https://www.nature.com/articles/s41572-021-00269-y ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2785514/ Minimal<<1000~4000https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4943081/ See also: https://www.nature.com/articles/ncomms11398; https://doi.org/10.1111/jgs.16027 Impaired autophagy, inflammation, protein aggregation, vascular agingAGE accumulation, cellular senescence, epigenetic changes, ER stress, immunosenescence (reduced clearance of pathogens), metabolic dysfunction, mitochondrial dysfunctionhttps://doi.org/10.1016/S1474-4422(15)70016-5 ; https://www.jci.org/articles/view/158453 ; https://pubmed.ncbi.nlm.nih.gov/30530798 ; https://doi.org/10.1111/febs.14332 ; https://pubmed.ncbi.nlm.nih.gov/30936558/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6355252/ ; https://www.nature.com/articles/s41419-022-05153-5 5.8 million (2020, out of 329.5 million Americans)CDC 7.6 years (but dependent on age at diagnosis)No interventions to treat underlying disease. Cholinergic agents used to improve impaired cognitive function but don't halt progress of disease.Cognitive and functional measures, MRI imaginghttps://doi.org/10.1016/S2666-7568(21)00140-9 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6061129/; https://alzres.biomedcentral.com/articles/10.1186/s13195-014-0087-9; 614332032452235501636533972168205421933https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9066743/2Grey mouse lemurs recapitulate some featuresNonhuman primates (esp. macaques), dogs https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5253109/pdf/nihms839392.pdf; https://alz-journals.onlinelibrary.wiley.com/doi/full/10.1002/trc2.1211431 (brain)$305 billionhttps://aaic.alz.org/downloads2020/2020_Facts_and_Figures_Fact_Sheet.pdf
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BrainVascular dementiaSmall vessel dementia, hypoperfusion dementia, multi-infarct dementia, hereditary vascular dementia, mixed dementiaCerebral blood flow assays (e.g. laser speckle flowmetry); neuropsychological testing; imaging (PET, CT, MRI, multiphoton); histologyCognitive function; blood-based biomarkers; imagingStrokes (recurrent or acute), hemorrhages, loss of BBB permeability, general breakdown of the cerebrovascular system - etiology is unclearhttps://www.ncbi.nlm.nih.gov/labs/pmc/articles/PMC2685259 ; https://doi.org/10.1016/S0140-6736(15)00463-8 ; https://www.ncbi.nlm.nih.gov/labs/pmc/articles/PMC3058404/ MinimalNo dataNo datahttps://www.alz.org/alzheimers-dementia/facts-figures Inflammation, vascular aging (arterial stiffness, microvascular rarefaction, narrowing of blood vessels)Cellular senescence, ER stress, impaired autophagy, mitochondrial dysfunction, oxidative stresshttps://doi.org/10.1016/j.arr.2016.09.007 ; https://doi.org/10.1002/jcp.27332 ; https://www.hindawi.com/journals/omcl/2015/504678/ 1.9 millionhttps://www.hindawi.com/journals/bmri/2014/908915/6.5 years (but dependent on age at diagnosis)NoneCognitive and functional measureshttps://doi.org/10.1016/S2666-7568(21)00140-9 ; https://www.ahajournals.org/doi/10.1161/jaha.117.0055681220462237462540521840805195215210349543https://www.ahajournals.org/doi/full/10.1161/JAHA.117.0055681.5Dogs recapitulate some featuresDogs, nonhuman primateshttps://doi.org/10.1186/s12916-017-0793-9 (see Table 1 for breakdown of specific animal models)Although less prevalent than AD, VaD costs more per patient https://doi.org/10.1016/S0022-510X(02)00257-5; https://www.ahajournals.org/doi/10.1161/01.STR.0000017878.85274.44
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BrainParkinson'sIdiopathic, early-onset, familialBehavioral and motor tests (e.g. locomotor activibity, gait analysis, grip strength), imaging (e.g. dopamine transporter levels)Medical history; neurological examination; CSF and blood biomarkers (e.g. alpha-synuclein species); imaging (e.g. dopamine transporter levels); responsiveness to levo-DOPA
Degeneration of dopaminergic neurons in the midbrain that are part of the basal ganglia—>not enough dopamine; degeneration of noradrenergic neurons; presence of Lewy bodies. Molecular mechanisms of pathogenesis largely unknown. Certain genetic mutations/variants and environmental risk factors are associated with susceptibility to PD, however this is a multifactorial disease so studies altering only one factor typically do not replicate the etiology of PD.https://link.springer.com/article/10.1007/s10654-011-9581-6 ; https://www.ncbi.nlm.nih.gov/books/NBK536725/ Minimal6.2 (M), 5.1 (F)140.7 (M), 78.4 (F)https://www.researchgate.net/publication/10734381_Incidence_of_Parkinson's_Disease_Variation_by_Age_Gender_and_RaceEthnicity (note: 2003, small sample size. For age 50, averaged stats for 40-49 and 50-59) ER stress, impaired autophagy, inflammation, mitochondrial dysfunction, protein aggregationAGE accumulation, cellular senescence, oxidative stress, telomere attritionhttps://doi.org/10.1016/j.freeradbiomed.2017.10.379 ; https://movementdisorders.onlinelibrary.wiley.com/doi/pdf/10.1002/mds.27037 ; https://www.sciencedirect.com/science/article/pii/S0753332221001128 ; https://doi.org/10.1016/j.tins.2014.02.010 ; https://doi.org/10.1111/ene.12252 ; https://doi.org/10.1002/mds.21867 ; https://www.sciencedirect.com/science/article/pii/S0753332221001128 ; https://www.frontiersin.org/articles/10.3389/fnins.2019.00560/full ; https://doi.org/10.1155/2013/239854 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7698446/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6355252/0.9 million (2020)Parkinson's FoundationPD is a progressive neurodegenerative disorder in which patients can do well for a number of years with dopamine-related drugs to boost or replace dopamine. Dopamine drugs do little to alleviate non-motor symptoms, which may appear before motor symptoms, and include constipation, disrupted sleep, and depression.No interventions to alter underlying degenerative process; treatment centered on reducing effect of distressing symptoms e.g. levodopa to increase dopamine levels, deep brain stimulation, along with non-drug therapies like exerciseFunctional scores (UPDRS, Hoehn and Yahr); self-administered questionnaire; wearables e.g. Parkinson’s Kinetigraph; balance testshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC6142835/41018142439202737152450224277103249419https://content.iospress.com/download/journal-of-parkinsons-disease/jpd219006?id=journal-of-parkinsons-disease%2Fjpd219006; https://www.nature.com/articles/nrd.2018.1361.5None known (possibly because of shorter lifespan of most other species)Nonhuman primates e.g. macaqueshttps://www.hindawi.com/journals/pd/2011/658083/; https://febs.onlinelibrary.wiley.com/doi/full/10.1111/j.1742-4658.2012.08491.x; https://onlinelibrary.wiley.com/doi/pdf/10.1002/bies.10067?casa_token=0-wZWMg0m48AAAAA:5oWeHL_2u9jMxQokdpO0bPMZMyMAsYtbnJZU24gRXT9ZbLcTmN_Jo-prHs3FVINYRCkKlrGy7n_XWkNR 2$25.4 billionhttps://www.nature.com/articles/s41531-020-0117-1
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BrainFrontotemporal dementiaNeuropsychological testing; imaging (PET, CT, MRI, multiphoton); biomarkers in CSF and blood; histologyDifferential diagnosis via behavioral change progression; family history and genetic testing; neuropsychological testing; bloodwork; imaging (MRI, FDG-PET, CT)Sporadic or genetic. Possibly: TAR DNA-binding protein; mutations in progranulin gene, C9orf72, and other less common geneshttps://www.sciencedirect.com/science/article/pii/S0140673615004614?casa_token=yjteX4uRpPQAAAAA:oUiNj5jtFVAogdB4LzUIgFXFgc5GOrcLCU-gdfDbqO8vETNBmvZI0UK424BP2pU5hrn7zwF0glXK; https://www.sciencedirect.com/science/article/pii/S1474442210702994?casa_token=3IUZ8NP1wucAAAAA:WjjKlDhOWFITefhwknUMqj0zqSmla2633_wTurTZ6LOtkf4XhwOm6BeSJQqUHMtYfymFxAqSX9fS; https://www.science.org/doi/full/10.1126/science.1134108?casa_token=b0QBXUwWSS0AAAAA%3AUnb6NCgFvrOzTw_szrqSQUHUgeRo8zs6VN6BJ6lXZTglmnKunxO7HtzMiN8zPwGguRfO4IhrYvG07TQT; https://www.nature.com/articles/nature05016; https://www.nature.com/articles/nature05017; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2892118/#R14 Minimal1.3414.95https://alzres.biomedcentral.com/articles/10.1186/s13195-020-00753-9/tables/1 ; see also https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3983262/ Inflammation, impaired autophagy, mitochondrial dysfunction, protein aggregationhttps://www.nature.com/articles/s41582-019-0231-z ; https://doi.org/10.1093/brain/awu138 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3243049/ 1.5 millionhttps://www.mayoclinic.org/diseases-conditions/frontotemporal-dementia/symptoms-causes/syc-203547377.6 years (but dependent on age at diagnosis)No interventions to treat the actual disease; treatment centered on reducing effect of distressing symptoms e.g. SSRIs and antipsychotics to aid mood and reduce psychosis, aggressive behavior, agitationFunctional measures; neuropsychological scores; cortical volume; white matter integrityhttps://doi.org/10.1016/S2666-7568(21)00140-9 ; https://www.sciencedirect.com/science/article/pii/S0140673615004614?casa_token=yjteX4uRpPQAAAAA:oUiNj5jtFVAogdB4LzUIgFXFgc5GOrcLCU-gdfDbqO8vETNBmvZI0UK424BP2pU5hrn7zwF0glXK; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3038533/; https://www.aafp.org/afp/2010/1201/p1372.html; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6351779/ 2136593144693443641216341834524373203https://www.nature.com/articles/s41582-020-0330-x1.5None knownNonhuman primateshttps://www.nature.com/articles/s41593-018-0236-81Similar to VaD, FTD is less prevalent than AD but more expensive per patient https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5711509/
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BrainStrokeIschemicHistology; MRI; functional and neurological measures (e.g. Bederson score)Imaging (CT, MRI); laser Doppler flowmetry; bloodwork; angiography; ECG; functional analysisBlood clot in cerebral artery -> ischemic cascade (increased oxidative stress, mitochondrial disfunction, induction of inflammatory processes) -> infarctionhttps://doi.org/10.1111/j.1747-4949.2008.00187.x; https://doi.org/10.1016/S0006-8993(01)03270-X ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3229752/< 31 (M), 26 (F)< 201 (M), 142 (F)546 (M), 482 (F)https://www.ahajournals.org/doi/10.1161/STROKEAHA.120.028910 Inflammation, vascular agingCellular senescence, oxidative stresshttps://www.nature.com/articles/nrneurol.2016.125 ; https://www.nature.com/articles/s41380-021-01361-1 0.7 million / yearCDC >5 yearsIntravenous thrombolysis (for patients presenting up to 4.5 hours after symptom onset); mechanical thrombectomy/clot extraction (for patients selected by imaging presenting up 24 hours after symptom onset). Secondary preventation after ischemic stroke: Single or dual antiplatelet therapy (aspirin + P2Y12 inhibitor); Anticoagulants; HMG-CoA reductase inhibitors (statins); blood pressure control; lifestyle modification (treatments depend on results of evaluation and specific risk factors present)Functional measures (e.g. modified Rankin scale, Barthel index, National Institute of Health Stroke Scale)https://doi.org/10.1016/S1474-4422(20)30101-0; https://doi.org/10.1161/STROKEAHA.118.02291314395216314826526923355918491101656565,135https://doi.org/10.1080/13543784.2022.2072725 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7276937/2.5Rats e.g. spontaneously hypertensive stroke-prone rat (SHRSP), dogsNonhuman primates (to lesser degree: pigs, dogs, sheep, rats)Rats often preferred to mice because they are easier to imagehttps://doi.org/10.1016/j.brainresbull.2016.02.016; https://www.understandinganimalresearch.org.uk/news/10-years-of-rat-research-how-stroke-studies-have-evolved; https://www.ahajournals.org/doi/full/10.1161/STROKEAHA.117.017112N/A4 (heart and stroke)$169.6 billionhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC8105541/
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BrainStrokeHemorrhagicRupture of blood vessel -> hematoma, increase in intracranial pressure -> secondary injury caused by inflammation, disruption of BBB, ROShttps://www.mayoclinic.org/diseases-conditions/stroke/diagnosis-treatment/drc-20350119; https://bestpractice.bmj.com/topics/en-us/1079; https://www.ncbi.nlm.nih.gov/books/NBK559173/0.1 million / yearCDC 1 monthNone routine; surgical evacuation for minority with infratentorial hemorrhage, oral nimodipine for sub-arachnoid hemorrhage33364516303843498612305620406891360610ICH: https://www.sciencedirect.com/science/article/pii/S2352396422000640 ; https://link.springer.com/article/10.1007/s12975-020-00830-z ; https://doi.org/10.1016/j.ebiom.2019.06.012 ; https://link.springer.com/article/10.1007/s11910-021-01144-9 ; SAH: https://www.ahajournals.org/doi/full/10.1161/STROKEAHA.119.025997$66.1 billionhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC8105541/
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HeartHeart failureReduced ejection fraction (systolic)Histology; echocardiography; MRI; hemodynamicsElectrocardiography; blood oxygen level; hemodynamics (bloodflow eg stroke volume)Reduced ability to pump blood, linked to cardiomyocyte death and loss of force/pumping (cell-cell coordinated coupling involved) and fibrosisConsultingMinimal1402000 (M), 1400 (F)https://academic.oup.com/eurheartj/article/25/18/1614/400157#89260333 (2004, incidence at 50-59, 75-79 respectively)ECM stiffening, vascular agingImpaired autophagy, inflammation, metabolic dysfunction, mitochondria dysfunction, oxidative stress https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6588179/ ; https://www.ahajournals.org/doi/10.1161/CIRCRESAHA.117.311082 ; https://www.nature.com/articles/s41569-019-0315-x 6.2 million (2020)CDC<4 yearsMultiple drugs: angiotensin converting enzyme (ACE) inhibitor, angiotensin II receptor blocker (ARB), beta‐blockers, angiotensin receptor‐neprilysin inhibitor (ARNI), mineralocorticoid receptor antagonist (MRA), digitalis, diuretics, hydralazines, nitrates, SGLT-2 inhibitors, CRT, hemodynamically guided management. For later stages, implanted devices like defibrillators. End stage: heart transplant.Ultimate endpoint: Reduction in mortality or rehospitalizationhttps://doi.org/10.1016/j.jacc.2017.08.074; https://www.acc.org/latest-in-cardiology/journal-scans/2017/11/10/22/18/heart-failure-with-preserved-borderline-aha-20173112914213427406018404823561292237133,588https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6348963/; https://doi.org/10.1080/13543784.2019.15513572.5None knownPigs, dogs (more secondary blood vessel formation than humans), mice, catsLarge animal models are ~$10khttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC7452204/N/A$30.7 billionhttps://www.ajmc.com/view/heart-failure-population-health-considerations
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HeartHeart failurePreserved ejection fraction (diastolic)Reduced intake of blood caused by myocyte hypertrophy and stiffness, fibrosis reduce heart function.ConsultingMRA (spironolactone), sacubitril/valsartan, SGLT-2 inhibitors, hemodynamically guided management.Ultimate endpoint: Reduction in mortality or rehospitalization
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CardiovascularAtherosclerosisHistology; morphology (esp. size of atherosclerotic lesion); imaging (MRI)Blood lipid profile (LDL cholesterol); blood pressure; medical history (risk factors e.g. smoking)Chronic inflammation due to lipid retention->development of lesions/plaques that break down, causing blood clot to form and occlude the arterial lumenhttps://www.ncbi.nlm.nih.gov/books/NBK507799/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5785239/ ; https://www.nature.com/articles/s41586-021-03392-8<1000700033000 (M), 30500 (F)*South Korea, https://bmcpublichealth.biomedcentral.com/articles/10.1186/s12889-019-7439-0/figures/2 Cellular senescence, immunosenescence, inflammation, mitochondrial dysfunctionER stress, oxidative stress, telomere attritionhttps://www.ahajournals.org/doi/full/10.1161/CIRCRESAHA.111.261388 ; https://academic.oup.com/cardiovascres/article/79/3/360/610497 ; https://www.nature.com/articles/s41569-020-0431-7 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5785239/ ; https://doi.org/10.1161/CIRCRESAHA.110.224766 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5112585/ 4.6 million https://www.omicsonline.org/united-states/atherosclerosis-peer-reviewed-pdf-ppt-articles/#:~:text=The%20Statistics%20for%20the%20extrapolated,4.6%20million%20people%20in%20USA.Moderately improved if risk factors (e.g. high blood pressure, LDL cholesterol) managed; bad if atherosclerosis results in condition like heart failure. Anti-inflammatory therapies recently shown to have some benefit and under further evaluation. Coronary angioplasty, coronary artery bypass surgery, statins to lower LDL cholesterol and increase HDL cholesterol, anticoagulants, antiplatelet medicines, blood pressure medicines, diabetes medicinesIncreased blood flow in arterieshttps://www.cell.com/fulltext/S0092-8674(01)00238-0, https://www.ncbi.nlm.nih.gov/books/NBK507799/ 163038183052224364218610732821491525807,106https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7901406/2.5Monkeys and pigs when fed high fat, high cholesterol dietsNonhuman primates, dogs, pigshttps://academic.oup.com/cardiovascres/article/79/3/360/610497, https://www.frontiersin.org/articles/10.3389/fcvm.2019.00046/full#B5, https://www.frontiersin.org/articles/10.3389/fcvm.2019.00046/full#B5, Li et al. 2011, https://www.cell.com/fulltext/S0092-8674(01)00238-0 1$330 billion*https://www.ahajournals.org/doi/full/10.1161/CIR.0000000000000558?rfr_dat=cr_pub++0pubmed&url_ver=Z39.88-2003&rfr_id=ori%3Arid%3Acrossref.org#d3e119149
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LiverNon-alcoholic steatohepatitisPatients (loosely) separated by fibrosis stage, F1-4Mainly histological assessment of fibrosis, steatosis, and immune infiltration. ALT/AST levels in blood, transcriptomics also usedImaging (esp. MR elastography); ALT/AST blood levels; liver biopsy; non-invasive tests (NITs)Hepatocyte death, with accumulation of toxic lipids and ER stress likely involved, leading to (mutually reinforcing) immune infiltration and stellate cells converting to fibrotic myofibroblasts. Well accepted as core framework, details being discussed. Clearly some genetic modifiers of disease risk. Dietary factors (glucose, fructose, saturated fatty acids) are important contributors.https://www.nature.com/articles/s41591-018-0104-9<150400480https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5866219/ER stress, inflammation, metabolic dysfunction (insulin resistance, hyperlipidemia)Cellular senescencehttps://www.nature.com/articles/s41591-018-0104-9 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3930975/17 million (2015)HepatologyHighly variable; order of 1/3 patients regress spontaneously, progressors usually decades to progress to cirrhosis and/or hepatocellular carcinoma. Elevated risk of cardiovascular events is strongest risk factor in NASH.Lifestyle modifications. End-stage: liver transplantationPhase 3: NAS and Fibrosis scoring systems for biopsy histology. Earlier/secondary measurements include non-invasive liver stiffness and adipocity, blood cholesterol, ALT/AST levels, sometimes inflammatory cytokines .https://doi.org/10.1002/hep.24376610201525354252552442754076139143178212Lots of candidates, but prominent failures in past few years. Most are focused on metabolism, some on fibrosis or inflammation. An FXR agonist came closest to approval, and is still a focus. Interestingly, most therapeutic failures are anti-inflammatory drugs (e.g., targeting ASK-1, CCR2/5, PDE4, caspases). Inflammation seemed like a good target but it may be that if we don't address the metabolic drivers, treating the consequences of lipotoxic injury to hepatocytes is not enough to stop and reverse disease. Reviews: https://www.nature.com/articles/s41575-020-00408-y ; https://www.tandfonline.com/doi/full/10.1080/13543784.2020.1721169 ; https://doi.org/10.1080/13543784.2020.1668926 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9062842/ 2.5Some do when on 'Western diet' (high fat, high sugar, high cholesterol). Female mice are very resistant to diet-induced NASH so most studies are in male mice.Primates are favored by pharma (although some discount animal models entirely)Many CROs exist for these modelshttps://www.sciencedirect.com/science/article/pii/S1521691811000308N/A1 (liver)$103 billionhttps://doi.org/10.1016/j.jhepr.2020.100142
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LiverCirrhosisCompensatedEnd stage of liver fibrosis caused by excessive immune response to chronic liver disease. Liver injury triggers transdifferentiation of hepatic stellate cells to myofibroblasts, which produce excess deposition of ECM characterizing fibrosis.https://www.sciencedirect.com/science/article/pii/S149938721830095X#fig0002; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3583179/ECM imbalance, inflammationCellular senescence, mitochondrial dysfunction, oxidative stresshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC4736713/ ; https://www.jci.org/articles/view/30542 0.6 million (2015) Journal of Clinical Gastroenterology9-12 yearsLifestyle modifications; treatment of symptoms e.g. non-selective beta-blockers to treat portal hypertension, diuretics for ascites and edema, lactulose and rifaximin for hepatic encephalopathyPhase 3: survival; Phase 2: CTP or MELD score, biomarkers e.g. inflammatory cytokines, oxidized albumin, NGALhttps://my.clevelandclinic.org/health/diseases/15572-cirrhosis-of-the-liver; https://www.fda.gov/media/127738/download515311925351419289101826601551001603062Nonhuman primates$7.4 billionhttps://journals.lww.com/ctg/Fulltext/2019/07000/Increasing_Economic_Burden_in_Hospitalized.12.aspx
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LiverCirrhosisNon-compensated2 yearsAs above; end stage: liver transplanthttps://doi.org/10.1016/j.jhep.2020.08.009
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LiverHepatocellular carcinomaHistology; imaging (CT, MRI, ultrasound, PET, optical)Serum AFP; imaging (esp. CT, MRI); occasionally biopsy[most frequently] Hepatitis, chronic liver disease, alcohol abuse, non-alcoholic fatty liver disease etc->cirrhosis->metabolic and oxidative injury->cyclical inflammation, necrosis, and repeated compensatory regeneration->genetic errors/mutations, telomere erosion, telomerase reactivation, chromosomal gains, activation of protooncogeneshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC5063561/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5490340/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2023919/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4145097/Minimal17.3 (M), 4.9 (F)65.2 (M), 30.3 (F)SEER Incidence Rates by Age at Diagnosis (2015-2019, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, inflammationECM imbalance (excessive production)https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5490340/0.04 million annual cases (2020)Journal of Clinical Oncology<1 years for patients with advanced disease; longer in earlier stagesSurgical resection, liver transplantation, transarterial chemoembolization, transarterial radiation, ethanol injection, percutaneous local ablation, microwave ablation, combination immunotherapy regimens (atezolizumab+bevacizumab or durvalumab+tremelimumab or nivolumab+ipilimumab) or tyrosine kinase inhibitors (lenvatinib, sorafenib, cabozantinib, ramucirumab) or anti-VEGF therapies (ramucirumab)Overall survival; time to recurrence; time to progression / progression-free survival; objective response ratehttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC5063561/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3989948/; https://aasldpubs.onlinelibrary.wiley.com/doi/full/10.1002/hep.27443 325067345177536486192766173365376533702https://www.nature.com/articles/nrd.2018.146; https://jeccr.biomedcentral.com/articles/10.1186/s13046-021-01968-w3.5Possibly mice, woodchuck models for HBV cirrhosisNonhuman primateshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC4800979/; https://www.nature.com/articles/labinvest2012155; https://onlinelibrary.wiley.com/doi/full/10.1111/j.1600-0684.2003.00048.x?casa_token=l3PmH6PquGkAAAAA%3AaeuJdEEvnhdSbq9pQ_AwHZlZm52daHuOjUh-RTyn1V7sKFy3EIG8eDlnsCAnn_qWno9CjlHAGP3pd6IX1$406 millionhttps://doi.org/10.1016/j.jhep.2008.07.029
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LungIdiopathic pulmonary fibrosisFibrosis (histology, enzymatic); lung function; immune infiltration; alveolar structureSpirometry; imaging (X-ray, CT); pulse oximetry and arterial blood gas analysis; bronchoscopy; lung biopsyEpithelial cell death -> inflammation and fibrosis, well supported but not completely understood(know from experience)Minimal6.2 (M), 5.4 (F)38.5 (M), 19.5 (F)https://www.atsjournals.org/doi/pdf/10.1164/rccm.200602-163OC (narrow case definition, incidence at 18-34, 45-54, 75+ respectively)Cellular senescence, impaired cell replacement, inflammation, telomere attritionDNA damage, ER stress, mitochondrial dysfunction, https://www.nature.com/articles/ncomms14532 ; https://www.sciencedirect.com/science/article/abs/pii/S2213260020303647 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7775527/ ; https://pubmed.ncbi.nlm.nih.gov/29567124/ 0.1 millionhttps://medlineplus.gov/genetics/condition/idiopathic-pulmonary-fibrosis/#:~:text=Idiopathic%20pulmonary%20fibrosis%20has%20an,sporadic%20form%20of%20the%20disease.3-4 yearsNintedanib, pirfenidone both improve QoL but not prognosisForced vital capacity; 6-min walk test; hospitalization; mortalityhttps://doi.org/10.1513/AnnalsATS.201706-423ED ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4162322/182630223650263246815293564174128274515https://www.nature.com/articles/nrd.2017.170; https://doi.org/10.1016/j.resinv.2020.04.0022Dogs, cats, donkeys get fibrosisFerrets, larger animals(know from experience) https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5532376/; https://doi.org/10.1165/rcmb.2017-0096ST; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3824038/12 (lung)>$3 billionhttps://www.ajmc.com/view/improving-outcomes-managing-costs-idiopathic-pulmonary-fibrosis
20
LungChronic obstructive pulmonary fibrosisFibrosis (histology, enzymatic); imaging (e.g. CT); lung function; immune infiltration; alveolar structureSpirometry (and other pulmonary function tests); imaging (X-ray, CT); pulse oximetry and arterial blood gas analysisChronic inflammation usually triggered by inhaled noxious gases (smoking in 85-90% of cases), which increase lung oxidative stress. There is also an excess ratio of proteases to antiproteases, leading to small airway fibrosis, lung parenchymal destruction (emphysema) and mucus hypersecretion (chronic bronchitis). Rare patients have genetic Alpha-1 deficiency which involves lack of antiproteases. https://www.lung.org/lung-health-diseases/lung-disease-lookup/copd/what-causes-copd#:~:text=It%20increases%20your%20risk%20of,men%20who%20have%20never%20smoked.Minimal800 (M), 300 (F)1700 (M), 600 (F)*Netherlands https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5005388/ Cellular senescence, inflammation, oxidative stress, telomere attritionImpaired autophagyhttps://pubmed.ncbi.nlm.nih.gov/33811810/, https://www.sciencedirect.com/science/article/pii/S135730391200031X?casa_token=WJJFyDWy4PAAAAAA:HjozMPX0ra7JiPPAi5qmtTg7vvLt-HZqVrZjPpkskHaCrbo91aG-AixfIlEA6CENefiYTgvqHgvq16.4 million (2018) https://www.lung.org/research/trends-in-lung-disease/copd-trends-brief/copd-prevalence5 years, reduces to 2 years for severe COPDInhaled long-acting bronchodilators, inhaled corticosteroids in selected patients, pulmonary rehab, supplemental oxygen, surgeryForced expiratory volume (FEV1); functional questionnaires (usually SGRQ); transition dyspnea index (TDI); time to first / frequency of / number of COPD exacerbation(s); mortalityhttps://www.emedicinehealth.com/ask_life_expectancy_for_copd/article_em.htm; https://doi.org/10.3389/fphar.2019.015193510691810152224325548972812276071,055https://www.nature.com/articles/nrd4254; https://doi.org/10.1002/cpt.1540; https://www.tandfonline.com/doi/abs/10.1080/13543784.2020.17690642None knownNone knownMice show pathophysiology but not structurally same as humans.https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2494776/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5414171/; https://www.karger.com/Article/FullText/5024891$30 billionhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC3694800/
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SystemicType 2 diabetesBlood glucose concentration, gulcose and insulin tolerance, histology (pancreas, liver, muscle), transcriptomicsBlood glucose concentration (average levels measured by glycated hemoglobin (A1C) test, random or fasting blood sugar tests also used); urine tests (presence of glucose?); serum insulin or c-peptide levels; occasionally imaging (ultrasound, MRI)Caused by two main factors: insulin resistance (IR) and defective insulin secretion by pancreatic beta-cells. IR -> increased blood sugar levels -> more insulin production in pancreas (hyperinsulinemia) and amyloid deposition + genetic susceptibility -> deficient insulin secretion from beta-cells -> hyperglycemiahttps://doi.org/10.3390/ijms21176275; https://doi.org/10.2337/dc12-1805; https://www.sciencedirect.com/science/article/pii/B97801281135300004393201010580https://www.cdc.gov/diabetes/data/statistics-report/newly-diagnosed-diabetes.htmlAGE accumulation, deregulated nutrient sensing (hyperactivation of mTOR), metabolic dysfunction (insulin resistance), inflammationCellular senescence, ER stress, mitochondrial dysfunction, oxidative stress, protein aggregation (amylin)https://www.hindawi.com/journals/omcl/2016/1810327/ ; https://link.springer.com/article/10.1007/s11010-014-2236-7 ; https://www.science.org/doi/10.1126/science.1104343 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4492843/ ; https://doi.org/10.1016/j.mad.2018.03.010 ; https://doi.org/10.1210/endocr/bqab136 ; https://doi.org/10.3389/fendo.2021.650158 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4477358/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3903318/ 34 million (2019)CDCAge dependent. ~7 years for those diagnosed at 75.Diet and exercise to maintain target blood sugar level; usually metformin, often acarbose (outside US), possibly DPP-4 inhibitors, GLP-1 receptor agonists, or SGLT-2 inhibitors, occasionally sulfonylureas, glinides, thiazolidinediones; possibly insulin therapy; possibly bariatric surgeryHbA1c (change from baseline); time to hyperglycemia rescue; fasting plasma glucose, insulin, c-peptide (change from baseline); body weight; postprandial blood glucose profilehttps://www.mayoclinic.org/diseases-conditions/type-2-diabetes/diagnosis-treatment/drc-20351199, clinicaltrials.gov35109132016223124335459150291285492822https://doi.org/10.1080/17460441.2020.17910782.5Cats, some pig strains, nonhuman primatesNonhuman primates (e.g. high fructose-fed rhesus monkeys), pigs, dogshttps://www.sciencedirect.com/science/article/pii/B9780128113530000439; https://doi.org/10.1093/ilar.47.3.186; https://diabetesjournals.org/diabetes/article/65/9/2700/40154/Pancreatic-Cells-From-Mice-Offset-Age-Associated22$237 billionhttps://www.diabetes.org/about-us/statistics/cost-diabetes
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Bone/jointOsteoporosisPost-menopausal (type 1), senile (type 2)Bone mineral density test via dual-energy x-ray absorptiometry (DXA) and micro-CT; bone turnover biomarkers for formation (e.g. serum osteocalcin and P1NP), resorption (e.g. C-terminal telopeptides) and osteoclast number (e.g. TRACP); histology (static and dynamic histomorphometry)Bone mineral density test via DXA; Physical exam to check for height/weight loss, posture changes, balance and gait, muscle strength (can you stand from sitting without using your arms?); Quantitative ultrasound of the heel to test for bone loss (after which, DXA if necessary); Fracture Risk Assessment Tool (FRAX)Imbalance between bone resorption and formation rates: increased rate of bone turnover possibly due to shortening of osteoblast lifespan and elevation or maintenance of osteoclast activityhttps://www.cell.com/cell-stem-cell/fulltext/S1934-5909(21)00010-2?_returnURL=https%3A%2F%2Flinkinghub.elsevier.com%2Fretrieve%2Fpii%2FS1934590921000102%3Fshowall%3Dtrue; https://www.bones.nih.gov/health-info/bone/osteoporosis/overview; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4534332/https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5335887/; https://www.sciencedirect.com/science/article/pii/S0025619611622143?casa_token=hBK10mgD0n8AAAAA:qCRm4o2qierQXZrIzvcFgHeU6H13M8HlKPrO-EYQ2QC0Qd1ykEsdKL4TA-j8VAK18CSlvxl5vNeW; https://www.sciencedirect.com/science/article/pii/S1530891X20412121?casa_token=GZ6MuL5nR60AAAAA:e-AnD3B2re7lngT1DlBvTf1JApYe7BiOe17RnBIBiJ4VGnNwABtZiRYVokj-MMionDmTGJP4mWMQ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5768298/ ; https://doi.org/10.1080/13547500601070842 No data2,247 (M), 2,313 (F)4,718 (M), 6,616 (F)https://asbmr.onlinelibrary.wiley.com/doi/10.1002/jbmr.2072 - see also: https://journals.plos.org/plosone/article?id=10.1371/journal.pone.0244291Cellular senescence, DNA damage, impaired cell replacement, metabolic dysfunction, mitochondrial dysfunctionImpaired autophagy, telomere attritionhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC8037620/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6816306/ ; https://www.nature.com/articles/nm.4385 ; https://pubmed.ncbi.nlm.nih.gov/32669663/ 10 million (2010)https://health.gov/healthypeople/about/workgroups/osteoporosis-workgroup#:~:text=In%20the%20United%20States%2C%20an,at%20increased%20risk%20for%20osteoporosis.Age dependent. Men treated at age 55 years or younger or women treated at age 70 years or younger have an average 15 years life expectancy.Pharmacological: Bisphosphonates (e.g. Alendronate, Risendronate) or Denosumab injections; Exercise; Good nutrition; Teriparatide (PTH 1-34), Evenity (monoclonal antibody against Sclerostin)Bone mass and bone strengthhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC5768298/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5335887/ ; https://asbmr.onlinelibrary.wiley.com/doi/10.1002/jbmr.24785810223876223760264519846103239135332833https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5798872/2None knownNonhuman primates, pigs, sheep (to a degree), dogs (to a degree)https://link.springer.com/article/10.1007/s00586-008-0813-8; https://link.springer.com/article/10.1007/s00586-008-0813-8; https://asbmr.onlinelibrary.wiley.com/doi/full/10.1359/jbmr.080516 1N/A$22 billionhttps://link.springer.com/article/10.1007/s00198-010-1419-7
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Bone/jointOsteoarthritisHistology; structural imaging (CT, MRI, ultrasound); molecular imaging (PET, optical); omics (esp. transcriptomics, proteomics); pain/functional outcomes/biomechanics (e.g. gait, muscle strength, weight bearing, joint stiffness, joint strength)Physical examination; arthroscopy; synovial fluid sampling; imaging e.g. MRI, radiographs with Kellgren-Lawrence radiographic grading schemeInterplay between systemic (advanced age, female gender, certain ethnicities, genetics, developmental conditions) and local factors (obesity, knee injury, knee laxity) causing degradation of cartilatge, theckning of bone and some degree of inflammation in the joint lining.https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2920533; https://www.aafp.org/afp/2012/0101/p49.html ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7327515/ ; https://onlinelibrary.wiley.com/doi/full/10.1002/jor.23343 ; https://journals.sagepub.com/doi/full/10.1177/1947603511402665Minimal5,000 (M), 10,500 (F)17,500 (M), 26,000 (F)https://doi.org/10.1016/j.joca.2020.03.004AGE accumulation, ECM imbalance (low synthesis, high degradation), inflammationCellular senescence, mitochondrial dysfunction, oxidative stresshttps://doi.org/10.1016/S0140-6736(11)60243-2 ; https://pubmed.ncbi.nlm.nih.gov/33208917/ ; https://www.jci.org/articles/view/95147 ; https://www.nature.com/articles/nm.4324 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5525396/32.5 million (2014)OA ActionDepends on which joints are affected, and to what degree—some patients are unaffected, others experience severe disability.Non-pharmacological: exercise, weight loss, braces, cranes, insoles; Pharmacological: Paracetamol/acetaminophen, NSAIDs, hyaluronic acid injections, glucocorticoid injections; Surgical: joint replacement surgeryPain and disability reductionhttps://www.ncbi.nlm.nih.gov/books/NBK482326/; https://www.aafp.org/afp/2012/0101/p49.html 6142610152112162317345750122291235376606https://doi.org/10.1016/j.bcp.2019.02.0343Many including mice, guinea pigs, dogs, sheep, goats, cows, horsesHorse, nonhuman primates; no single "gold standard" modelhttps://www.sciencedirect.com/science/article/pii/S1063458416304782;
https://www.sciencedirect.com/science/article/pii/S1063458412000544;
https://www.sciencedirect.com/science/article/pii/S1063458406003244; https://journals.sagepub.com/doi/full/10.1177/0300985815588611
12 (arthritis)$16.5 billionhttps://www.cdc.gov/arthritis/data_statistics/cost.htm
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Bone/jointRheumatoid arthritisSeropositive (positive for Rheumatoid Factor) or SeronegativeHistology; radiographic imaging; blood tests (CRP level, RF and anti-CCP antibodies); urinary excretion rates of joint destruction biomarkers (HP and LP)Radiographic imaging; blood tests (ESR, CRP level, RF and anti-CCP antibodies)Genetic susceptibility (including human leukocyte antigen (HLA) alleles), epigenetic modifications (e.g. DNA methylation at EXOSC1), and environmental risk factors (e.g. smoking, bacteria, EBV infection) trigger (in a manner incompletely understood) the citrullination of antigens -> activation of antigen presenting cells (APCs), migration to lymph nodes -> formation of autoantibodies (ACPAs and RF), migration to joint tissue -> inflammation of synovial membrane (synovitis), angiogenesis and pannus -> cartilage and bone destruction, joint damage. RA is 2-3x more prevalent among females, perhaps due to immune stimulating effects of estrogen.https://journals.sagepub.com/doi/full/10.1177/0300985815588612; https://www.frontiersin.org/articles/10.3389/fimmu.2022.887460/full; https://pubmed.ncbi.nlm.nih.gov/11001374/ ; https://pubmed.ncbi.nlm.nih.gov/28451788/ ; https://www.nature.com/articles/nrdp201814.0 (M), 12.6 (F)28 (M), 66 (F)81 (M), 122 (F)https://academic.oup.com/rheumatology/article/56/5/736/2864858Immunosenescence, inflammationCellular senescence, telomere attritionhttps://pubmed.ncbi.nlm.nih.gov/26212057/ ; www.ncbi.nlm.nih.gov/pmc/articles/PMC263838/ 1.5 million (2007)Arthritis FoundationAge dependent. Average 26.3 years life expectancy after diagnosis.Depends of length of RA history: NSAIDs, steroids, csDMARDs, tsDMARDs (JAKi), biological agentsPain and improved physical function; decreased global assessment of disease activityhttps://www.mayoclinic.org/diseases-conditions/rheumatoid-arthritis/diagnosis-treatment/drc-20353653; https://onlinelibrary.wiley.com/doi/10.1002/art.415976152714202622324919326370152274127359637https://link.springer.com/article/10.1007/s00281-017-0623-3 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7500842/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8179789/2None knownNonhuman primates, pigs (immune system more closely aligned than NHPs)https://www.frontiersin.org/articles/10.3389/fimmu.2019.00203/full or https://www.karger.com/Article/FullText/508239#ref124 or https://www.nature.com/articles/ncprheum0973 or https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1789807/ or https://translational-medicine.biomedcentral.com/articles/10.1186/s12967-020-02402-z ; 1$19.3 billionhttps://pubmed.ncbi.nlm.nih.gov/19908947/
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ReproductionMenopauseHormone levels (esp. FSH, estrogen, progesterone); histology; cognitive (e.g. Moris water maze tests)Usually diagnosed by presentation of symptoms (e.g. vasomotor, irregular periods); FSH and estradiol levels Ovarian dysfunction and hypothalamic-pituitary-ovarian feedback loop desensitization to estrogen leading to decrease in follicle number and insensitivity of remaining follicles to estrogen which triggers ovulation. Also hypothesis that aging of the central control of ovulation in the hypothalamus might have a role. https://www.mayoclinic.org/diseases-conditions/menopause/symptoms-causes/syc-20353397 ; https://www.nice.org.uk/guidance/ng23/chapter/Recommendations#diagnosis-of-perimenopause-and-menopause ; https://journals.lww.com/grh/Fulltext/2018/06000/The_etiology_of_menopause___not_just_ovarian.1.aspxMinimalAverage age at menopause is 51Minimalhttps://my.clevelandclinic.org/health/diseases/21138-premature-and-early-menopause#:~:text=Premature%20menopause%20happens%20to%20about,in%20about%205%25%20of%20women.AGE accumulation, cellular senescence, DNA damage, epigenetic changes, ER stress, inflammation, mitochondrial dysfunction, oxidative stress, telomere attritionhttps://academic.oup.com/humupd/article/28/2/172/6464146 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4995944/ ; https://doi.org/10.1093/humrep/det383 ; https://pubmed.ncbi.nlm.nih.gov/26629734/ ; https://pubmed.ncbi.nlm.nih.gov/27562289 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3952404/ 50 million (2020)North American Menopause SocietyHighly variable, but age dependent. Those with early menopause live 3.5 years longer than those with late menopause.Hormone replacement therapy (including tibolone, estrogen +/- progestin/SERM); for vaginal symptoms: vaginal estrogen / DHEA / oral ospemiphene testosterone for postmenopausal HSDDSymptomatic relief; prevention of osteoporosishttps://www.mayoclinic.org/diseases-conditions/menopause/diagnosis-treatment/drc-20353401 ; https://www.clinicaladvisor.com/home/topics/ob-gyn-information-center/early-menopause-associated-with-shorter-life-expectancy-early-diagnosis-of-type-2-diabetes/241318315016233723335660104249257514780Mainly dietary supplements and behavioural intervention, few compounds in trials https://www.clinicaltrials.gov/ct2/results?cond=menopause&term=&cntry=&state=&city=&dist= 1Whales i.e KillerRhesus macaqueNo other species gets menopause other than 4 species of whale. Rhesus macaque maintain cycles till death but pattern does change.https://www.science.org/content/article/study-suggests-surprising-reason-killer-whales-go-through-menopause OR https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2553520/#:~:text=Reproductive%20senescence%20has%20been%20more,age%20%5B38%2C%2039%5D 1N/A>$100 millionhttps://womensmentalhealth.org/posts/the-immense-burden-of-menopausal-symptoms/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5620512/
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EyeAge-related macular degeneration"Wet AMD"Histology; imaging (e.g. fundus photography, optical coherence tomography (OCT), electron microscopy); omics (esp. transcriptomics, proteomics); Miles assay of vascular permeabilityAge-Related Eye Disease Study (AREDS) classification; retinal imaging (e.g. fundus fluorescein angiography, fundus autofluorescence imaging, near-infrared reflectance, optical coherence tomography)Interference with Vascular Endothelial Growth Factor (VEGF) function-->cessation of vascular growth, neovascular regression, dysregulation of the complement systemhttps://www.sciencedirect.com/science/article/pii/S0140673612602827?casa_token=Q2FARXQvV64AAAAA:2wQ6j89eOByoFhFw67u8ZnwMM7dKRf3QS-nZ8S1yN73d4BnPQxbwKgzlZSq6bg4G0N04pRt6gTay; https://pubmed.ncbi.nlm.nih.gov/35122134/; https://www.nejm.org/doi/full/10.1056/NEJMoa054481; https://journals.sagepub.com/doi/abs/10.1177/1120672119857896 Minimal20 (M), 10 (F) 490 (M), 320 (F)490 (M), 320 (F)https://www.sciencedirect.com/science/article/pii/S0002939415001919Cellular senescence, DNA damage, inflammationMitochondrial dysfunctionhttps://www.sciencedirect.com/science/article/pii/S0140673612602827?casa_token=Q2FARXQvV64AAAAA:2wQ6j89eOByoFhFw67u8ZnwMM7dKRf3QS-nZ8S1yN73d4BnPQxbwKgzlZSq6bg4G0N04pRt6gTay; https://journals.lww.com/internat-ophthalmology/Citation/2021/06140/Gene_Therapy_in_the_Treatment_of_Geographic.19.aspx; https://iovs.arvojournals.org/article.aspx?articleid=2164895 11 million (2020)https://www.brightfocus.org/sources-macular-degeneration-facts-figuresPoor; disease is chronic and progressive, leads to more severe vision loss than dry AMDLaser photocoagulation (rarely used), photodynamic therapy (rarely used), VEGF inhibitors, visual rehabilitationVisual gains, visual stabilisation, improved reading ability and mobilityhttps://www.sciencedirect.com/science/article/pii/S0140673612602827?casa_token=Q2FARXQvV64AAAAA:2wQ6j89eOByoFhFw67u8ZnwMM7dKRf3QS-nZ8S1yN73d4BnPQxbwKgzlZSq6bg4G0N04pRt6gTay; https://www.sciencedirect.com/science/article/pii/S0161642007002333?casa_token=Eo8rqx3HVRQAAAAA:QyLxxKBT0Yg-8a52kJxX42g5bpuz39_Lv3EjHYThVjCH6iCk9HIkx; https://www.nejm.org/doi/full/10.1056/NEJMoa054481 DbX7bh2PWr7AakyPNEkK-UB 1418331627372734481340503086156241382674https://doi.org/10.1016/j.drudis.2022.04.013; https://doi.org/10.1111/bph.154593Cynomolgus monkeys"Nonhuman primates are the only animals with a retinal structure closely resembling that found in humans, most notably the presence of a macula". Pig eyes are the closest to humans of the nonhuman primates. No single animal model develops all the signs of AMD in a progressive manner. Several are good for certain facets of the disease: Simian primates (drusen development); mice (changes in Bruch membrane, inflammation; retinal pigment epithelium and photoreceptor loss)https://www.sciencedirect.com/science/article/pii/S0002944010644276?casa_token=juH5857x8OEAAAAA:FoylCq2gME4Xrm5ebpic4o6SGtuz09sWoHRtU1U79QifukEJ2paUxqXNEUk4lS1sowvWJ_wpoyL0; https://www.sciencedirect.com/science/article/pii/S004269890700329X; https://iovs.arvojournals.org/article.aspx?articleid=2164895; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4186726/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4186726/; https://www.sciencedirect.com/science/article/pii/S0098299712000635?casa_token=UxuTRi4pNMYAAAAA:oB5N0fD12__MvfhN-r7VYWzRze4vIiR6paYJB7EVWQR5b_O2AW3DCiCLrfZxb2pdeSCXf4s5SEQ3; https://www.nature.com/articles/nm950; https://www.sciencedirect.com/science/article/pii/S0024320521007980?casa_token=wPIjv8zfhXAAAAAA:MtBwms-qcspa-SpwOp6t6g9W2Sr69d37qdCjNUXVb9UPv6irXxvxxmfAzT0zdfzTLXSRYpB23NIE 12 (eye diseases)$600 millionhttps://www.brightfocus.org/macular/article/age-related-macular-facts-figures
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EyeAge-related macular degeneration"Dry AMD"Unclear, but possibly intrinsic and extrinsic stressors of the poorly regenerative retinal pigment epithelium, e.g. oxidative stress caused by the high metabolic demand of photoreceptors, photo-oxidation, and environmental stressors such as cigarette smoke. Certain genetic mutations, dysregulation of the complement system, mitochondrial dysfunction, inflammation are also associated with dry AMD.https://www.sciencedirect.com/science/article/pii/S0140673612602827?casa_token=Q2FARXQvV64AAAAA:2wQ6j89eOByoFhFw67u8ZnwMM7dKRf3QS-nZ8S1yN73d4BnPQxbwKgzlZSq6bg4G0N04pRt6gTay; https://pubmed.ncbi.nlm.nih.gov/24433969/; Richard et al. 2021; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5424580/; https://www.aaojournal.org/article/S0161-6420(13)00942-1/fulltext Poor; disease is chronic and progressive; half of patients develop dry AMD in both eyes within 7 years of initial diagnosisNone as yet; some evidence for dietary interventions for slowing disease progressionChange in geographic atrophy area, visual gains, visual stabilisation, improved reading ability and mobilityhttps://www.sciencedirect.com/science/article/pii/S0140673612602827?casa_token=Q2FARXQvV64AAAAA:2wQ6j89eOByoFhFw67u8ZnwMM7dKRf3QS-nZ8S1yN73d4BnPQxbwKgzlZSq6bg4G0N04pRt6gTay; https://www.sciencedirect.com/science/article/pii/S016164201932353X; https://pubmed.ncbi.nlm.nih.gov/24433969/; Arabi and Shahraki 2021; Richard et al. 2021; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5424580/; https://www.aaojournal.org/article/S0161-6420(13)00942-1/fulltext; https://www.aaojournal.org/article/S0161-6420(17)30968-5/fulltext; https://www.nature.com/articles/s41467-018-04175-y https://www.sciencedirect.com/science/article/pii/S0002944010644276?casa_token=juH5857x8OEAAAAA:FoylCq2gME4Xrm5ebpic4o6SGtuz09sWoHRtU1U79QifukEJ2paUxqXNEUk4lS1sowvWJ_wpoyL0; https://www.sciencedirect.com/science/article/pii/S004269890700329X; https://iovs.arvojournals.org/article.aspx?articleid=2164895; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4186726/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4186726/; https://www.sciencedirect.com/science/article/pii/S0098299712000635?casa_token=UxuTRi4pNMYAAAAA:oB5N0fD12__MvfhN-r7VYWzRze4vIiR6paYJB7EVWQR5b_O2AW3DCiCLrfZxb2pdeSCXf4s5SEQ3; https://www.nature.com/articles/nm950; https://www.sciencedirect.com/science/article/pii/S0024320521007980?casa_token=wPIjv8zfhXAAAAAA:MtBwms-qcspa-SpwOp6t6g9W2Sr69d37qdCjNUXVb9UPv6irXxvxxmfAzT0zdfzTLXSRYpB23NIE
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EyeGlaucomaPrimary open-angle, primary closed-angleIntraocular pressure measurement (tonometry), ocular blood flowTonometry, visual field test, pachymetry, gonioscopy, imaging esp. optical coherence tomography (OCT)Primary open-angle glaucoma: intraocular pressure-induced stress and strain->mechanical axonal damage and disruption of axonal transport->interrupted retrograde delivery of essential trophic factors to retinal ganglion cells->degeneration of retinal ganglion cells->higher intraocular pressure; other factors, including blood flow and ischemia may have role. Primary closed-angle glaucoma: [most commonly] resistance to aqueous humor flow->acqueous humor accumulates behind iris->iris convexity increases->angle closurehttps://www.nature.com/articles/nrdp201667; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4523637/, https://www.sciencedirect.com/science/article/pii/S0039625707001889?casa_token=JIvjTDOelGMAAAAA:uWOlBPjJQthtZUBfKdDEArnC_rUHXxrxDg61-TL6QUL8fr4YUA6kCT0w2WWEfr9KIy6fW7Dy4pxS , https://www.sciencedirect.com/science/article/pii/S1350946220301051 Minimal110370https://iovs.arvojournals.org/article.aspx?articleid=2161444DNA damage, mitochondrial dyfunction, oxidative stresshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC2526097/ ; https://doi.org/10.1016/j.survophthal.2007.08.011 ; https://doi.org/10.1016/j.exer.2010.07.015 3 million (2004)Glaucoma Research FoundationPrimary open-angle glaucoma: Vision loss is permanent, actual blindness is uncommon, majority of patients maintain useful vision through their lifetime, but a significant proportion loses vision resulting in driving ineligibility or partial sight certification; Primary closed-angle glaucoma: blindness is more commonProstaglandin analogues, beta-blockers, diuretics, cholinergic agonists, alpha agonists, rho kinase inhibitors, argon laser trabeculoplasty, selective laser trabeculoplasty, micropulse laser trabeculoplasty, laser peripheral iridotomy, laser iridoplasty, trabeculectomy, glaucoma drainage implants, nonpenetrating glaucoma surgery, microinvasive glaucoma surgery, incisional glaucoma surgeryLower intraocular pressurehttps://www.sciencedirect.com/science/article, https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4523637, https://www.nature.com/articles/6702284 4514591712172724305546102171190420643https://doi.org/10.1080/14728214.2022.21102402Some rodents, monkeysNonhuman primateshttps://www.sciencedirect.com/science/article/pii/S001448350800434X?casa_token=yqdkrISwCCsAAAAA:WSqf_TwU_ZHHQSsayW827AzWy0GRHyVhbErHRtf6bQwtNqKhTXLYat1iCl0IIkwP_o6jpLJmGzSz#bib36, John 2005; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3364028/ 1$2.9 billionhttps://pubmed.ncbi.nlm.nih.gov/17159036/
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EyeDiabetic retinopathyNon-proliferative, proliferativeHistology (e.g. trypsin digest), omics (e.g. genomics, transcriptomics, proteomics), ocular blood flow, retinal inflammation biomarkers (e.g. TNF-alpha and ICAM-1), electrophysiological testing, imaging (fundus photography (FP), fundus fluorescein angiography (FFA) and optical coherence tomography (OCT))FP; FFA; OCT; OCT-AngiographyHyperglycemia due to diabetes induces microangiopathy in the retina, which results in increased vascular permeability of blood-retinal barrier and leakage. Accumulation of fluid in the macula due to breakdown of the blood-retinal barrier can cause vision loss (diabetic macular edema). Apoptosis of pericytes and endothelial cells results in capillary occlusion and retinal ischemia, increasing VEGF levels which promote neovascularization. https://journals.biologists.com/dmm/article/5/4/444/3291/Update-on-animal-models-of-diabetic-retinopathy; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5518557/pdf/jciinsight-2-93751.pdf; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3380708/17,460 (M), 12, 070 (F) *26,160 (M), 10,810 (F)13,690 (M), 5,850 (F)*Taiwan, 2011 (ages 20-39, 40-59, 60-79 respectively) doi:10.1001/jamaophthalmol.2014.859Inflammation, metabolic dysfunction, oxidative stressAGE accumulation, mitochondrial dysfunctionhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC8289197/pdf/cia-16-1367.pdf ; https://journals.biologists.com/dmm/article/5/4/444/3291/Update-on-animal-models-of-diabetic-retinopathy ; https://doi.org/10.1371/journal.pone.0139664 ; https://www.mdpi.com/2079-7737/8/2/31/htm ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3951818; 4.1 million (2004)JAMA OpthamologyDepends on stage. For review of prognostic models, see: https://www.nature.com/articles/s41433-018-0322-xLaser photocoagulation; surgical vitrectomy; intraocular injections of steroids and VEGF inhibitors, combined VEGF and Ang2 inhibitors, steroid implants (Iliuvien, and Ozurdex)Visual acuity, diabetic retinopathy severity score (DRSS), OCT central macular thickness, OCT biomarkers such as DRILhttps://www.nature.com/articles/s41433-018-0322-x; https://journals.biologists.com/dmm/article/5/4/444/3291/Update-on-animal-models-of-diabetic-retinopathy13325730334728417572533203686270466819https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7061411/3Pigs, dogsPigs, dogs, nonhuman primates, zebrafish (cheaper but less similar, hyperglycemia is induced)https://link.springer.com/article/10.1007/s11892-017-0913-0; https://jbiomedsci.biomedcentral.com/articles/10.1186/1423-0127-20-38; https://journals.biologists.com/dmm/article/5/4/444/3291/Update-on-animal-models-of-diabetic-retinopathy; https://www.hindawi.com/journals/jdr/2013/106594/1$500 millionhttps://pubmed.ncbi.nlm.nih.gov/17159036/
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Skin/hairAlopecia (hair loss)AndrogeneticDuration of hair cycles (e.g. via contrast-enhanced phototrichogram); area of hair regrowth; hair weight, density, length, shaft diameterScalp examination; trichoscopy; standardized scalp global photographyAGA stems from a combination of genetic and hormonal factors. Male AGA is a substantially (~80%) hereditary trait with polygenic origin. Dihydrotestosterone (DHT), which is metabolized from testosterone by 5-alpha reductase, has a high affinity for the androgen receptor (AR). DHT is thought to produce follicle miniaturization, but how this occurs and why it is opposite to the effect of androgens on hair follicles in other areas e.g. beard, axillary, pubic hair is unsettled. Variation of the AR gene (which resides on the X chromosome) accounts for about 40% of AGA heritability. https://doi.org/10.1002/der2.58; https://www.ncbi.nlm.nih.gov/books/NBK278957/; https://journals.lww.com/jewds/Fulltext/2013/09000/Androgenetic_alopecia__update_on_epidemiology,.1.aspx; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4174066/No dataNo dataNo datahttps://pubmed.ncbi.nlm.nih.gov/9865198/Impaired cell replacementDNA damage, inflammation, oxidative stresshttps://www.ncbi.nlm.nih.gov/books/NBK278957/ ; https://doi.org/10.1002/der2.58 ; https://doi.org/10.1111/j.1468-3083.2008.02937.x 80 millionhttps://medlineplus.gov/genetics/condition/androgenetic-alopecia/#frequencyNo significant effect on life expectancyTopical minoxidil; 5-alpha reductase inhibitors (e.g. finasteride); occasionally low level laser therapy, hair transplant surgeryHair count, hair growth, hair fiber diameterhttps://www.uspharmacist.com/article/treatment-options-for-androgenetic-alopecia ; https://journals.lww.com/jewds/Fulltext/2013/09000/Androgenetic_alopecia__update_on_epidemiology,.1.aspx 4912121720121621203242334895115161353Oral minoxidil, anti-prolactin monoclonal antibody injection, topical prostaglandin. See: https://doi.org/10.1080/13543784.2019.1568989 1.5Bears, lions, nonhuman primatesNonhuman primates esp. stump-tailed macaquehttps://onlinelibrary.wiley.com/doi/full/10.1046/j.1365-2230.2002.01086.x; https://onlinelibrary.wiley.com/doi/full/10.1002/ski2.151N/AEstimate not foundhttps://www.aafp.org/pubs/afp/issues/1999/0415/p2189.html
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Bladder cancerBladder cancerNon-muscle invasive (NMIBC), muscle invasive (MIBC)Histology; imaging (CT, MRI, ultrasound, optical); gene expression; bladder weight measurementCystoscopy; bladder sonography; urine cytopathology; transurethral resection; imaging (X-ray, CT, MRI, ultrasound)Genetic and epigenetic changes around tumor suppressor genes and oncogenes of unclear origin, exacerbated by carcinogens. Papillary tumors characterized by activating mutations in FGFR2, non-papillary bladder cancer involves inactivation of tumor suppressors including TP53 and RB1. https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2957872/; https://www.oncotarget.com/article/17714/text/Minimal11.9131.3https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, male female combined, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, epigenetic changes (hypermethylation of tumor suppressors)Inflammationhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC2957872/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5696263/ ; https://pubmed.ncbi.nlm.nih.gov/24818724/ 0.7 million (2019)NCI77% 5 year relative survival rateSurgery (transurethral resection of bladder tumor, cystectomy); intravesical therapy (immunotherapy with BCG or chemotherapy); radiation; systemic chemotherapy; IV infusions of immune checkpoint (PD-1 and PD-L1) inhibitors; FGFR inhibitors e.g. erdafitinibResponse rate and duration; event free survival (time to recurrence, progression); urine markers? https://www.cancer.org/cancer/bladder-cancer/treating.html ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5321095/ ; https://www.fda.gov/media/101468/download ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4832566/pdf/blc-1-2-blc150016.pdf ; clinicaltrials.gov 3251714362874347581726124214058304542802https://www.nature.com/articles/nrd.2016.141; https://doi.org/10.1080/14712598.2022.20828692.5Some rat strains (e.g. Brown Norway and DA/Han), dogsDogshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC5593682/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6036476/14 (all cancers)$9.4 billionhttps://progressreport.cancer.gov/after/economic_burden
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Breast cancerBreast cancerLuminal A, luminal B, luminal B-like, HER-2 enriched, triple negativeHistology; imaging (PET, MRI, high frequency ultrasound, optical); omics (esp. DNA methylation, genomics, transcriptomics); hormone levels; apoptosis assays (e.g. TUNEL)Local breast biopsy (occasionally also fine needle aspiration) and bilateral breast imaging using mammography (ie. low dose radiography, ultrasonography, and occasionally digital breast tomosynthesis); MRI and PET scanning may also be used to complement imaging and look for local or distant tumor spread.The primary risk factors for breast cancer (beyond age) are genetic and hormone (i.e. estrogen) related. Most breast cancers are associated with multiple, low-penetrant genetic mutations and epigenetic alternations inhibiting DNA repair pathways, growth control mechanisms and chromosomal stability, but about 10% of breast cancers are induced by germline inheritance of a highly penetrant loss-of-function mutation in a tumor-suppressing gene such as BRCA1 and BRCA2. Nearly 80% of breast cancers are characterized by their overexpression of steroid hormone receptors (ER, PR) and/or amplification of the human epidermal growth factor receptor-2 (HER2) gene. For 70-80% of breast cancers, estrogen promotes and drives breast cancer growth by binding ER, which is a ligand-activated TF that transcriptionally enhances cell proliferation. Up to 20% of breast cancers have amplified HER2 (also referred to as ERBB2), which encodes a membrane-localized receptor tyrosine kinase that when overexpressed is constitutively activated to drive uncontrolled cell proliferation, cell survival, local invasiveness and distant metastasis. Triple-negative breast cancers (those that do not overexpress ER, PR or HER2) are the most common type of breast cancer associated with inherited BRCA1 related mutations. https://www.nature.com/articles/s41572-019-0111-2; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3681186/ ; https://link.springer.com/article/10.1007/s00432-010-0957-x ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6778915/10.3 (F)229.8 (F)461.1 (F)https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, epigenetic changes (global hypomethylation, hypermethylation of tumor suppressors)Inflammationhttps://www.nature.com/articles/s41572-019-0111-2 ; https://doi.org/10.3390/cancers13153918 ; https://www.mdpi.com/1422-0067/19/4/1166/htm 3.7 million (2019)NCI91% 5 year relative survival rateSurgery, radiation (usually EBRT, sometimes brachytherapy); for estrogen or progesterone-receptor positive cancers: hormone therapy (selective estrogen receptor modulators e.g. tamoxifen, selective estrogen receptor degraders, aromatase inhibitors, ovarian suppression), CDK4/6 inhibitors, mTOR inhibitor, PI3K inhibitor (for those with PIK3CA mutation); HER2 monoclonal antibodies or kinase inhibitors for HER2-positive cancer; PARP inhibitors for those with BRCA mutation; antibody-drug conjugate for triple negative cancers (ER-, PR-, HER2-); immune checkpoint (PD-1) inhibitors. Event free survival (time to recurrence, progression); overall survival; response rate and duration; percentage change in tumor sizehttps://www.nature.com/articles/s41572-019-0111-2 ; https://www.cancer.org/cancer/breast-cancer/treatment.html ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3237237/ ; https://ascopubs.org/doi/full/10.1200/edbk_280451 294466415783538011717335433601192264881,006https://www.nature.com/articles/d41573-021-00018-6; https://doi.org/10.1016/j.ctrv.2017.11.0032.5Cats and dogs frequently develop spontaneous BC; rodents rarely develop spontaneous mammary cancers during their lifespan unless genetically engineered to do soCats, dogs, pigsTransgenic mice for BC research generally are 200-300 USD per subject (Jackson Laboratory), while transgenic pigs (e.g., the Oncopig) can be in the range of 1-2K USD. Per diem, drug and labor costs also ~order of magnitude higher.https://www.frontiersin.org/articles/10.3389/fonc.2022.788038/full#T2; https://www.sciencedirect.com/science/article/pii/B97801241589480004032$29.8 billionhttps://progressreport.cancer.gov/after/economic_burden
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GastrointestinalColorectal cancerCMS1 (immune), CMS2 (canonical), CMS3 (metabolic), CMS4 (mesenchymal)Histology; imaging (e.g. optical, ultrasound); omics (esp. DNA methylation, genomics, transcriptomics)Guaiac fecal occult blood or fecal immunochemical tests, sigmoidoscopy, colonoscopy, CT scanGenetic and epigenetic mutations (including mutations leading to DNA replication errors, oncogene activation and tumor suppressor inactivation) allow colonic epithelium to develop precancerous lesions that can form invasive carcinoma. ~70% of colon cancer is sporadic, while ~30% of patients have family history, of which a third is caused by known inherited syndromes including familial adenomatous polyposis and Lynch syndromehttps://www.nature.com/articles/nm.3967; https://www.ncbi.nlm.nih.gov/books/NBK470380/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7795459/pdf/ijms-22-00200.pdf3.462.7169https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, male female combined, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, epigenetic changes (hypermethylation of tumor suppressors, global hypomethylation), inflammationMitochondrial dysfunction, telomere attritionhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC7795459/pdf/ijms-22-00200.pdf ; https://clinicalepigeneticsjournal.biomedcentral.com/track/pdf/10.1186/s13148-019-0801-3.pdf ; https://www.sciencedirect.com/science/article/pii/S0748798319309266#! ; https://www.nature.com/articles/s41577-021-00534-x ; https://doi.org/10.1016/j.dld.2018.02.009 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3934464/ 1.4 million (2019)NCI65% 5 year relative survival rateEndoscopic or surgical resection; ablation or embolization; radiation therapy; chemotherapy; IV-infused monoclonal antibodies targeting VEGFs (vascular endothelial growth factors) and EGFR (epidermal growth factors receptor); BRAF inhibitors (for those with BRAF mutation); immune checkpoint (PD-1, CTLA-4) inhibitors Response rate and duration; event free survival (time to recurrence, progression); overall survival; percentage change in tumor sizehttps://www.cancer.org/cancer/colon-rectal-cancer/treating.html; clinicaltrials.gov26345233507034527820328839691212925871,067https://www.nature.com/articles/nrd.2017.59 ; https://www.nature.com/articles/s41575-019-0126-x 3Mice, dogs, sheepDogs, nonhuman primates (e.g. cotton-top tamarin)https://pubmed.ncbi.nlm.nih.gov/23076650/; https://pubmed.ncbi.nlm.nih.gov/33916402/1$24.3 billionhttps://progressreport.cancer.gov/after/economic_burden
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ReproductionEndometrial CancerPOLE mutated, microsatellite instability, copy number low, copy number highHistology; imaging (e.g. MRI, CT, optical, ultrasound); omics (esp. DNA methylation, genomics, transcriptomics)Pelvic exam; ultrasound; hysteroscopy; biopsy; dilation and curettage; CA-125 blood levelMolecular basis largely unclear and subtype-dependent, but hormonal imbalance (esp. high proportion of estrogen to progesterone) thought to stimulate endometrial proliferation and hyperplasia -> atypical premalignant lesions -> endometrioid carcinoma with oncogene mutations (CTNNB1, KRAS, and POLE), tumor suppressor mutations (in PTEN) and defects in DNA mismatch repair.https://www.ncbi.nlm.nih.gov/books/NBK525981/; https://www.mdpi.com/1422-0067/22/17/9274/htm2.1 (F)48.1 (F)91.9 (F)https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, epigenetic changes (hypermethylation of tumor suppressors)Inflammation, metabolic dysfunction (insulin resistance), mitochondrial dysfunction, oxidative stresshttps://www.nature.com/articles/s41467-021-22560-y ; https://www.tandfonline.com/doi/full/10.4161/epi.5.6.12431 ; https://www.mdpi.com/1422-0067/19/7/2076/htm ; https://www.mdpi.com/2072-6694/12/9/2559/htm ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2966326/ 0.8 million (2019)NCI81% 5 year relative survival rateSurgery; radiation (brachytherapy or external beam); for late stage: chemotherapy, hormone therapy (progestins, anti-estrogen drugs like tamoxifen, luteinizing hormone-releasing hormone agonists, aromatase inhibitors), targeted drugs (kinase inhibitors, angiogenesis inhibitors, mTOR inhibitors)Event free survival (time to recurrence, progression); response rate and duration; overall survival;https://www.cancer.org/cancer/endometrial-cancer/treating.html; NCI4346614354827091117244182293754117377548https://www.nature.com/articles/d41573-022-00016-2; https://www.nature.com/articles/nrd.2017.922.5Rodents (esp Donryu rats)Nonhuman primateshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC6121384/pdf/ijms-19-02348.pdf1$5.8 billionhttps://progressreport.cancer.gov/after/economic_burden
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KidneyKidney CancerRenal cell carcinoma (clear cell, papillary, chromophobe, clear cell papillary, collecting duct, medullary), urothelial carcinoma, sarcoma, lymphoma, Wilm's tumor (primarily in children)Histology; imaging (e.g. optical, MRI); apoptosis assay (e.g. flow cytometry); omics (esp. DNA methylation, genomics, transcriptomics); tumor weightImaging (CT scan, MRI, ultrasound); biopsy; urianalysis (blood in urine?) + bloodwork (number of red blood cells)Unclear, but like other cancers, genetic and epigenetic changes around tumor suppressor genes and oncogenes are implicated e.g. loss of chromosome 3p, inhibition of VHL seen in >90% of cases of clear cell renal cell carcinoma (most common type of kidney cancer)https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5850086/pdf/f1000research-7-14298.pdf1.326.173.1https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, male female combined, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, epigenetic changes (hypermethylation of tumor suppressors)Deregulated nutrient sensing, telomere attrition, oxidative stresshttps://www.nature.com/articles/nrurol.2010.47 ; https://www.nature.com/articles/nrurol.2010.46 ; https://content.iospress.com/articles/kidney-cancer/kca190052#ref001%20ref002 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5069705/ ; https://jhoonline.biomedcentral.com/articles/10.1186/s13045-015-0180-y 0.6 million (2019)NCI77% 5 year relative survival rateSurgery; ablation; drugs targeting angiogensis (including sunitinib, sorafenib, pazopanib, cabozantinib, lenvatinib, bavcizumab, axitinib, tivozanib, belzutifan) or targeting mTOR protein (including temsirolimus, everolimus); immune checkpoint (PD-1, PD-L1, CTLA-4) inhibitors; occasionally cytokines (IL-1 and interferon-alfa); rarely radiation or chemotherapyResponse rate and duration; event free survival (time to recurrence, progression); overall survival; percentage change in tumor sizehttps://www.cancer.org/cancer/kidney-cancer/treating.html; NCI; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3176905/pdf/conc-18-s11.pdf4066934361915372992548133255396257541781https://doi.org/10.1016/j.ctrv.2018.07.0093RodentsZebrafish, dogshttps://www.sciencedirect.com/science/article/pii/S1936523319306394#bb04151$9.7 billionhttps://progressreport.cancer.gov/after/economic_burden
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BloodLeukemiaChronic lymphocytic, acute myeloid, chronic myeloid, acute lymphocytic. (Acute = fast onset, associated with less mature hematopoietic precursor cells than chronic.)Complete blood count; flow cytometry; imaging (optical); omics (e.g. transcriptomics, genomics)Physical examination (pale skin from anemia, swelling of lymph nodes, and enlargement of liver and spleen); complete blood count (abnormal levels of red or white blood cells or platelets); flow cytometry; peripheral blood smear; bone marrow biopsy; lumbar punctureLeukemogenesis is subtype dependent, but generally involves somatic mutations, epigenetic modifications and chromosomal alterations that impair control of growth and division of hematopoietic precursor cells (blasts in the case of acute leukemias, or more mature cells in chronic leukemias) -> overcrowding in the bone marrow -> decreased number of red blood cells, platelets and white blood cells -> symptoms such as fatigue, thrombocytopenia, infection https://www.nature.com/articles/nrc2765.pdf; https://www.sciencedirect.com/science/article/abs/pii/S1521692603000860; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5333535/; https://www.nature.com/articles/nrdp201696; https://www.nature.com/articles/nrdp201610
2.911.966.5https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, male female combined, incidence at 25-29, 50-54, 75-79 respectively)Clonal hematopoiesis, DNA damage, epigenetic changes (hypermethylation of tumor suppressors)Inflammationhttps://doi.org/10.1016/j.molmed.2019.04.006 ; https://doi.org/10.3390/cancers12010103 ; https://doi.org/10.1007/s12185-014-1651-6 ; https://doi.org/10.1158/0008-5472.CAN-06-1681 0.5 million (2019)NCI66% 5 year relative survival rate (on average, but highly subtype dependent, better for chronic leukemias)Chemotherapy; targeted therapy; radiation; stem cell/bone marrow transplant; immunotherapy; CAR-T cell therapyResponse rate and duration; overall survival; event free survival (time to recurrence, progression)NCI; https://www.mayoclinic.org/diseases-conditions/leukemia/diagnosis-treatment/drc-20374378; https://acsjournals.onlinelibrary.wiley.com/doi/full/10.1002/cncr.30622; https://pubmed.ncbi.nlm.nih.gov/29524739/3350754669966078110203464264684173318539AML: https://doi.org/10.3390/cancers12113225 CLL: https://jhoonline.biomedcentral.com/articles/10.1186/s13045-021-01054-w CML: https://www.frontiersin.org/articles/10.3389/fonc.2019.00665/full 2Some rodents e.g. New Zealand black mice spontaneously develop chronic lymphocytic leukemiaDogs (rarely used), nonhuman primateshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC3568447/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6722578/; https://doi.org/10.3389/fonc.2017.000223$13.6 billionhttps://progressreport.cancer.gov/after/economic_burden
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LungLung CancerSmall cell, non-small cellHistology; imaging (CT, MRI, ultrasound); respiratory function (e.g. via plethysmography); omics (esp. DNA methylation, genomics, transcriptomics); tumor size, body weight, body temperatureLow dose CT; fine needle aspiration or core needle biopsy (often with CT or ultrasound guidance)Lung cancer can be divided into two main subtypes: small cell lung cancer (SCLC) and non-small cell lung cancer (NSCLC), which account for 15% and 85% of cases respectively. SCLC is a highly malignant tumor with strong links to tobacco, which causes the dual inactivation of two tumor suppressors, p53 and RB. Conversely, activating oncogenic mutations e.g. in EGFR are often responsible for tumorigenesis in NSCLC (although non-small cells may also have loss of tumor suppressors like p53 and RB).https://www.ncbi.nlm.nih.gov/labs/pmc/articles/PMC3864624/ ; https://www.nature.com/articles/nrdp20159 ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7218036/0.641.4380https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, male female combined, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, epigenetic changes (hypermethylation of tumor suppressors), oxidative stressInflammationhttps://www.sciencedirect.com/science/article/pii/S0092867421002907 ; https://doi.org/10.1016/j.freeradbiomed.2013.08.006 0.6 million (2019)NCI23% 5 year relative survival rateSurgery; chemoradiation; immunotherapy; targeted therapy (angiogenesis inhibitors, also KRAS, EGFR, ALK, ROS1, BRAF, RET, MET, NTRK inhibitors) Overall survival; progression-free survival; objective response rateNCI; https://www.fda.gov/media/116860/download; https://pubmed.ncbi.nlm.nih.gov/25806152/3244663853754569921738703562110305503792https://www.nature.com/articles/s41392-019-0099-9; https://www.nature.com/articles/d41573-020-00057-52.5Some mice strains, dogs, sheepSheep, dogs, nonhuman primateshttps://www.hindawi.com/journals/bmri/2015/621324/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2094362/; https://pubmed.ncbi.nlm.nih.gov/25991702/1$23.8 billionhttps://progressreport.cancer.gov/after/economic_burden
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Skin/hairMelanomaSuperficial spreading, nodular, lentigo, acral lentiginousHistology; imaging (optical, CT, PET, ultrasound); tumor size, body weight; omics (esp. genomics, transcriptomics, proteomics)Biopsy (assays include IHC, FISH, CGH, gene expression); imaging (reflectance confocal microscopy, Xray, ultrasound, CT, MRI, PET); blood levels of LDH Melanoma is characterized by genetic and epigenetic changes around tumor suppressor genes and oncogenes in melanocytes (skin cells producing melanin). Specifically, the majority of sporadic melanomas have activating mutations (e.g. BRAF and RAS genes) that lead to dysregulation of the MAPK pathway and increase cell proliferation. UV radiation exposure is a primary risk factor known to produce DNA strand breaks and ROS. Additionally, with ~10% of patients having family history, melanoma has a hereditary component, including germline mutations in CDKN2A and CDK4.https://www.cancer.org/cancer/melanoma-skin-cancer/detection-diagnosis-staging/how-diagnosed.html; https://www.nature.com/articles/nrdp20153; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4346328/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2897908/3.9 (M), 7.1(F)29.4 (M), 27.3 (F)154.2 (M), 55.3 (F)SEER Incidence Rates by Age at Diagnosis (2015-2019, incidence at 25-29, 50-54, 75-79 respectively)DNA damageImmunosenescence, inflammation, oxidative stresshttps://www.tandfonline.com/doi/full/10.1586/14737140.2015.961426 ; https://doi.org/10.1016/j.prp.2018.11.020 1.4 million (2019)NCI94% 5 year relative survival rateSurgery; radiation (brachytherapy or external beam); for late stage: immunotherapy (PD-1 inhibitors, PD-L1 inhibitor, CTLA-4 inhibitor, LAG-3 inhibitor); targeted therapy (kinase inhibitors, angiogenesis inhibitors, mTOR inhibitors); occasionally chemotherapy, hormone therapy (progestins, anti-estrogen drugs like tamoxifen, luteinizing hormone-releasing hormone agonists, aromatase inhibitors)Event free survival (time to recurrence, progression); response rate and duration; overall survival; percentage change in tumor sizehttps://aacrjournals.org/clincancerres/article/18/2/336/77325/New-Challenges-in-Endpoints-for-Drug-Development; https://www.cancer.org/cancer/melanoma-skin-cancer/treating.html; NCI3348794257784164832235127234497235435733https://www.nature.com/articles/d41573-022-00075-52.5Sharks, rabbits, horses, penguins, snakes, cows, goats, lions, alpacas, nonhuman primates... Horses, dogs, pigs, zebrafish, nonhuman primateshttps://onlinelibrary.wiley.com/doi/10.1002/path.5505; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4832391/pdf/PATH-238-152.pdf; https://www.nature.com/articles/s41684-019-0447-y1$5.7 billionhttps://progressreport.cancer.gov/after/economic_burden
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Lymphatic systemNon-Hodgkin LymphomaB-cell, T-cell, NK-cellHistology; imaging (PET, optical); omics (esp. transcriptomics, mutation profiling, proteomics)Imaging (CT, MRI, ultrasound, PET); biopsy (flow cytometry, immunohistochemistry, chromosome tests, NGS)Genetic mutations (point mutations or gene rearrangements) in lymphocytes (most commonly B cells, but also T cells) cause uncontrolled division and/or reduce apoptosis. NHL etiology remains poorly understood and varies across subtype, but risk factors include immune-altering conditions like autoimmune disorders (e.g. rheumatoid arthritis), viruses and infections (like HIV/AIDs, H. Pylori infection, EBV, HTLV-1, HCV), immunosuppressant drugs or inherited immune disorders (e.g. Wiskott-Aldrich syndrome), as well as chronic antigen stimulation. The formation of antigen receptors involves gene rearrangements, and errors (like the chromosomal translocations characterizing subtypes such as follicular lymphoma, mantle cell lymphoma and Burkitt lymphoma) can lead to activation of oncogenes. https://link.springer.com/chapter/10.1007/978-3-319-13150-4_1; https://europepmc.org/article/nbk/nbk559328; https://www.cancer.org/cancer/non-hodgkin-lymphoma/detection-diagnosis-staging/how-diagnosed.html3.320.998.7https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, male female combined, incidence at 25-29, 50-54, 75-79 respectively)DNA damageClonal hematopoesis, immunosenescence, inflammation, https://immunityageing.biomedcentral.com/track/pdf/10.1186/s12979-018-0130-y.pdf ; https://link.springer.com/article/10.1007/s11912-015-0457-x 0.8 million (2019)NCI74% 5 year relative survival rateRadiation therapy; chemotherapy; immunotherapy: monoclonal antibodies targetting B-or T-lymphocyte antigens (CD20, CD19, CD30, CD79b), CAR T-cell therapies; targeted therapy (kinase and BCL2 inhibitors); stem cell transplant Response rate and duration; Event free survival (time to recurrence, progression); overall survivalhttps://www.cancer.org/cancer/non-hodgkin-lymphoma/treating.html; NCI3862884979115428099315181274672140305439https://www.nature.com/articles/d41573-019-00051-62Dogs, nonhuman primates, genetically-engineered miceDogs, nonhuman primateshttps://onlinelibrary.wiley.com/doi/10.1002/hon.2017; https://www.frontiersin.org/articles/10.3389/fonc.2017.00022/full; https://www.hindawi.com/journals/ah/2012/701704/1$18.6 billionhttps://progressreport.cancer.gov/after/economic_burden
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PancreasPancreatic CancerExocrine, neuroendocrineHistology; imaging (ultrasound, MRI, optical); blood biomarkers (e.g. CA19)Blood biomarkers: CA19-9, CA-50, DUPAN-2, SPAN-1, CEA; imaging: contrast-enhanced multislice CT, MRI, endoluminal ultrasound with fine needle aspiration cytology; laparoscopy with laparoscopic ultrasoundGenetic and epigenetic alternations of oncogenes (esp. K-ras, which is activated in >90% of pancreatic cancers; as well as growth factors and P13K/Akt) and tumor suppressors (inactivation of p53, INK4a/ARF, BRCA2, Smad4); reactivation of developmental signalling (Notch and Hedgehog). Beyond age and race, risk factors include chronic pancreatitis, smoking, high alcohol intake, obesity and pesticides. https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1955499/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3319955/; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6396775/pdf/wjon-10-010.pdf0.412.181.7https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018, male female combined, incidence at 25-29, 50-54, 75-79 respectively)DNA damage, epigenetic changes (hypermethylation of tumor suppressors)Inflammationhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC1955499/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3319955/ ; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6396775/pdf/wjon-10-010.pdf 0.09 million (2019)NCI5-6 months; 12% 5 year relative survival rateSurgery; ablation or embolization; radiation; chemotherapy (including gemcitabine with nab-paclitaxel, FOLFIRINOX); EGFR inhibitor; PARP or NTRK inhibitors (for those with BRCA and NTRK mutations respectively); immunotherapy (PD-1 inhibitor)Objective response rate and duration; event free survival (time to recurrence, progression); overall survival; percentage change in tumor sizeNCI; https://www.frontiersin.org/articles/10.3389/fonc.2019.00144/full324267405681405072192736295095126405587https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7517959/3HamstersPigs, dogshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC3319955/; https://www.frontiersin.org/articles/10.3389/fonc.2019.00144/full; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6995380/; https://www.gastrojournal.org/article/S0016-5085(13)00190-X/fulltext2$2.7 billionhttps://doi.org/10.1016/j.pan.2020.09.002
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ReproductionProstate CancerAdenocarcinoma (acinar, ductal), transitional cell carcinoma, squamous cell carcinoma, small cellHistology; blood biomarkers (esp. PSA, genistein); imaging (e.g. optical, MRI); omics (esp. DNA methylation, genomics, transcriptomics); tumor weight and volumeBlood tests (esp. PSA levels); digital rectal examination; imaging (esp. MRI); prostate biopsyUnclear, but associated with somatic mutations in oncogenes or tumor suppressor genes in the prostate epithelial cell genome, commonly including TMPRSS2–ERG fusion, MYC amplification, PTEN and RB1 deletion and TP53 mutation. Also a hereditary component: approx. 9% of men with prostate cancer have family history, and germline mutations in DNA damage repair such as BRCA1 and BRCA2 are known to increase risk of early onset prostate cancer. https://www.clinicalkey.com/#!/content/book/3-s2.0-B9780323546423001506; https://www.nature.com/articles/s41572-020-00243-0
Minimal112 (M)572 (M)https://gis.cdc.gov/Cancer/USCS/#/Demographics/ (2018)DNA damage, epigenetic changesMitochondrial dysfunction, inflammation, oxidative stresshttps://www.pnas.org/doi/10.1073/pnas.0931396100 ; https://doi.org/10.1016/j.semcancer.2009.02.006 ; https://doi.org/10.1093/carcin/bgy133 ; https://doi.org/10.1016/j.bbcan.2008.11.001 ; https://link.springer.com/chapter/10.1007/978-3-319-95693-0_3 ; https://www.nature.com/articles/pcan201313 3.3 million (2019)NCI97% 5 year relative survival rateSurgery (prostatectomy, orchiectomy); radiation therapy (external beam, brachytherapy, radiopharmaceuticals targeting PSMA or bones); hormone therapy: androgen deprivation therapy (LHRH agonists "medical castration", LHRH antagonists), anti-androgens; PARP-inhibitors for those with BRCA mutation; chemotherapy; occasionally cryotherapy; cancer vaccine (Sipuleucel-T)Overall survival; metastasis-free survival; PSA levels (change, nadir, time to progression); testosterone (for LHRH agonists)https://doi.org/10.1016/S0090-4295(02)01585-6; https://journals.lww.com/journalppo/fulltext/2020/01000/surrogate_endpoints_in_localized_prostate_cancer.8.aspx; https://www.cancer.org/cancer/prostate-cancer/treating; NCI3039703856783361991837672847821583921,091https://www.nature.com/articles/d41573-021-00111-w2.5Some rat strains, dogsDogs, nonhuman primateshttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC3644021/; https://www.mdpi.com/2306-7381/1/1/16; https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3221286/1$22.3 billionhttps://progressreport.cancer.gov/after/economic_burden
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